ALPHA-KETOADIPIC ACIDURIA - DESCRIPTION OF A NEW METABOLIC ERROR IN LYSINE-TRYPTOPHAN DEGRADATION

被引:31
作者
WILSON, RW
WILSON, CM
GATES, SC
HIGGINS, JV
机构
[1] MICHIGAN STATE UNIV,DEPT NAT SCI,E LANSING,MI 48824
[2] MICHIGAN STATE UNIV,DEPT ZOOL,E LANSING,MI 48824
[3] MICHIGAN STATE UNIV,DEPT BIOCHEM,E LANSING,MI 48824
[4] MICHIGAN STATE UNIV,DEPT HUMAN DEV,E LANSING,MI 48824
关键词
D O I
10.1203/00006450-197506000-00002
中图分类号
R72 [儿科学];
学科分类号
100202 ;
摘要
引用
收藏
页码:522 / 526
页数:5
相关论文
共 21 条
[1]  
BLASS J P, 1970, Journal of Clinical Investigation, V49, P423, DOI 10.1172/JCI106251
[2]   ALPHA-KETOISOCAPROIC ACID INHIBITION OF PYRUVATE AND ALPHA-KETOGLUTARATE OXIDATIVE DECARBOXYLATION IN RAT LIVER SLICES [J].
BOWDEN, JA ;
BRESTEL, EP ;
COPE, WT ;
MCARTHUR, CL ;
WESTFALL, DN ;
FRIED, M .
BIOCHEMICAL MEDICINE, 1970, 4 (01) :69-&
[3]   SACCAROPINURIA - A NEW INBORN ERROR OF LYSINE METABOLISM [J].
CARSON, NAJ ;
SCALLY, BG ;
NEILL, DW ;
CARRE, IJ .
NATURE, 1968, 218 (5142) :679-&
[4]   QUANTITATIVE EXTRACTION AND GAS-LIQUID CHROMATOGRAPHIC DETERMINATION OF ORGANIC ACIDS IN URINE [J].
CHALMERS, RA .
ANALYST, 1972, 97 (1161) :958-967
[5]  
DANCIS J, 1972, METABOLIC BASIS INHE, P426
[6]   ALPHA-AMINOADIPIC ACIDURIA, A NON-DELETERIOUS INBORN METABOLIC DEFECT [J].
FISCHER, MH ;
GERRITSEN, T ;
OPITZ, JM .
HUMANGENETIK, 1974, 24 (04) :265-270
[7]  
GATFIELD PD, 1968, CAN MED ASSOC J, V99, P1215
[8]   GLUTARIC ACIDURIA - NEW DISORDER OF AMINO-ACID METABOLISM [J].
GOODMAN, SI ;
MARKEY, SP ;
MOE, PG ;
MILES, BS ;
TENG, CC .
BIOCHEMICAL MEDICINE, 1975, 12 (01) :12-21
[9]  
HIRASHIMA M, 1967, J BIOL CHEM, V242, P902
[10]   CELLULAR LOCALIZATION AND CHARACTERIZATION OF BOVINE LIVER BRANCHED-CHAIN ALPHA-KETO ACID DEHYDROGENASES [J].
JOHNSON, WA ;
CONNELLY, JL .
BIOCHEMISTRY, 1972, 11 (10) :1967-&