LIGNOCEROYL-COASH LIGASE - ENZYME DEFECT IN FATTY-ACID BETA-OXIDATION SYSTEM IN X-LINKED CHILDHOOD ADRENOLEUKODYSTROPHY

被引：153

作者：

HASHMI, M ^{[1
]}

STANLEY, W ^{[1
]}

SINGH, I ^{[1
]}

机构：

[1] MED UNIV S CAROLINA,DEPT PATHOL,CHARLESTON,SC 29425

来源：

FEBS LETTERS | 1986年 / 196卷 / 02期

关键词：

D O I：

10.1016/0014-5793(86)80256-3

中图分类号：

Q5 [生物化学]; Q7 [分子生物学];

学科分类号：

071010 ; 081704 ;

摘要：

引用

页码：247 / 250

页数：4

共 28 条

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BRONFMAN, M ;

INESTROSA, NC ;

NERVI, FO ;

LEIGHTON, F .

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[5] FATTY-ACID OXIDATION BY HUMAN-LIVER PEROXISOMES [J].

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INESTROSA, NC ;

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[6]

CHEN WC, 1982, J CELL BIOL, V95, pA452

[7]

FOLCH J, 1957, J BIOL CHEM, V226, P497

[8] PEROXISOMAL DEFECTS IN NEONATAL-ONSET AND X-LINKED ADRENOLEUKODYSTROPHIES [J].

GOLDFISCHER, S ;

COLLINS, J ;

RAPIN, I ;

COLTOFFSCHILLER, B ;

CHANG, CH ;

NIGRO, M ;

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MOSER, HW ;

LAZAROW, PB .

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[9]

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[10]

HOSHI M, 1973, J LIPID RES, V14, P406

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