HUMAN-MUSCLE PYRUVATE-DEHYDROGENASE ACTIVITY

被引:11
作者
EVANS, OB [1 ]
机构
[1] VANDERBILT UNIV,MED CTR,JERRY LEWIS NEUROMUSCULAR RES CTR,NASHVILLE,TN 37212
关键词
D O I
10.1212/WNL.33.1.51
中图分类号
R74 [神经病学与精神病学];
学科分类号
摘要
引用
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页码:51 / 56
页数:6
相关论文
共 24 条
[1]  
BARBEAU A, 1976, CAN J NEUROL SCI, V4, P379
[2]   PLASMA-INSULIN IN PATIENTS WITH MYOTONIC-DYSTROPHY AND THEIR RELATIVES [J].
BARBOSA, J ;
NUTTALL, EQ ;
KENNEDY, W ;
GOETZ, F .
MEDICINE, 1974, 53 (04) :307-323
[3]   LOW ACTIVITIES OF PYRUVATE AND OXOGLUTARATE DEHYDROGENASE COMPLEXES IN 5 PATIENTS WITH FRIEDREICHS ATAXIA [J].
BLASS, JP ;
KARK, RAP ;
MENON, NK .
NEW ENGLAND JOURNAL OF MEDICINE, 1976, 295 (02) :62-67
[4]   NORMAL PYRUVATE-DEHYDROGENASE COMPLEX ACTIVITY IN PATIENTS WITH FRIEDREICH ATAXIA [J].
CONSTANTOPOULOS, G ;
CHANG, CSC ;
BARRANGER, JA .
ANNALS OF NEUROLOGY, 1980, 8 (06) :636-639
[5]   DEFECTIVE ACTIVATION OF THE PYRUVATE-DEHYDROGENASE COMPLEX IN SUB-ACUTE NECROTIZING ENCEPHALOMYELOPATHY (LEIGH DISEASE) [J].
DEVIVO, DC ;
HAYMOND, MW ;
OBERT, KA ;
NELSON, JS ;
PAGLIARA, AS .
ANNALS OF NEUROLOGY, 1979, 6 (06) :483-494
[6]   PYRUVATE DECARBOXYLASE DEFICIENCY IN SUB-ACUTE NECROTIZING ENCEPHALOMYELOPATHY [J].
EVANS, OB .
ARCHIVES OF NEUROLOGY, 1981, 38 (08) :515-519
[7]  
EVANS OB, 1981, ANN NEUROL, V10, P86
[8]   NORMAL MUSCLE PYRUVATE OXIDATION IN SPINOCEREBELLAR DEGENERATIONS [J].
EVANS, OB .
ANNALS OF NEUROLOGY, 1981, 9 (01) :93-94
[9]  
GEOFFROY G, 1976, Canadian Journal of Neurological Sciences, V3, P279
[10]   GLUCOSE-METABOLISM IN PERFUSED SKELETAL-MUSCLE - PYRUVATE-DEHYDROGENASE ACTIVITY IN STARVATION, DIABETES AND EXERCISE [J].
HAGG, SA ;
TAYLOR, SI ;
RUDERMAN, NB .
BIOCHEMICAL JOURNAL, 1976, 158 (02) :203-210