STUDIES ON HUMAN N-ACETYL-BETA-D-HEXOSAMINIDASE-C SEPARATED FROM NEONATAL BRAIN

被引:32
作者
BESLEY, GTN [1 ]
BROADHEAD, DM [1 ]
机构
[1] ROY HOSP SICK CHILDREN,DEPT PATHOL,EDINBURGH EH9 1LF,SCOTLAND
关键词
D O I
10.1042/bj1550205
中图分类号
Q5 [生物化学]; Q7 [分子生物学];
学科分类号
071010 ; 081704 ;
摘要
引用
收藏
页码:205 / 208
页数:4
相关论文
共 21 条
[1]  
BEUTLER E, 1975, AM J HUM GENET, V27, P628
[2]   SEPARATION AND PROPERTIES OF HUMAN BRAIN HEXOSAMINIDASE C [J].
BRAIDMAN, I ;
CARROLL, M ;
DANCE, N ;
ROBINSON, D .
BIOCHEMICAL JOURNAL, 1974, 143 (02) :295-&
[3]   STUDIES ON HEXOSAMINIDASE C IN CULTURED SKIN FIBROBLASTS FROM PATIENTS WITH SANDHOFFS DISEASE [J].
BROADHEAD, DM ;
BESLEY, GTN .
BIOCHEMICAL SOCIETY TRANSACTIONS, 1975, 3 (02) :247-250
[4]   CYSTIC-FIBROSIS AND LIVER BETA-GALACTOSIDASE AND BETA-GLUCOSIDASE [J].
BUTTERWORTH, J ;
BAIN, AD ;
MCCRAE, WM .
CLINICA CHIMICA ACTA, 1972, 41 (01) :367-+
[5]   TAY-SACHS AND SANDHOFFS DISEASE - INTERGENIC COMPLEMENTATION AFTER SOMATIC-CELL HYBRIDIZATION [J].
GALJAARD, H ;
HOOGEVEEN, A ;
WITVERBE.HA ;
REUSER, AJJ ;
KEIJZER, W ;
WESTERVELD, A ;
BOOTSMA, D .
EXPERIMENTAL CELL RESEARCH, 1974, 87 (02) :444-448
[6]  
GODSON GN, 1970, ANAL BIOCHEM, V35, P66
[7]   PREPARATION OF BUFFERS FOR USE IN ENZYME STUDIES [J].
GOMORI, G .
METHODS IN ENZYMOLOGY, 1955, 1 :138-146
[8]  
HOOGHWIN.GJ, 1972, H-S Z PHYSIOL CHEM, V353, P839
[9]   N-ACETYL-BETA-D-HEXOSAMINIDASE COMPONENT-A - DIFFERENT FORMS IN HUMAN TISSUES AND FLUIDS [J].
IKONNE, JU ;
ELLIS, RB .
BIOCHEMICAL JOURNAL, 1973, 135 (03) :457-462
[10]  
IKONNE JU, 1975, AM J HUM GENET, V27, P639