PILOT SCALE PURIFICATION OF ALPHA-GALACTOSIDASE-A FROM COHN FRACTION-IV-1 OF HUMAN-PLASMA

被引:22
作者
BISHOP, DF
WAMPLER, DE
SGOURIS, JT
BONEFELD, RJ
ANDERSON, DK
HAWLEY, MC
SWEELEY, CC
机构
[1] MICHIGAN STATE UNIV, DEPT BIOCHEM, E LANSING, MI 48824 USA
[2] MICHIGAN STATE UNIV, DEPT CHEM ENGN, E LANSING, MI 48824 USA
关键词
D O I
10.1016/0005-2744(78)90109-2
中图分类号
Q5 [生物化学]; Q7 [分子生物学];
学科分类号
071010 ; 081704 ;
摘要
引用
收藏
页码:109 / 120
页数:12
相关论文
共 25 条
[1]  
BEUTLER E, 1972, J BIOL CHEM, V247, P7195
[2]  
BEUTLER E, 1971, J LAB CLIN MED, V78, P987
[3]   FLUOROMETRIC ASSAY OF PROTEINS IN NANOGRAM RANGE [J].
BOHLEN, P ;
STEIN, S ;
DAIRMAN, W ;
UDENFRIEND, S .
ARCHIVES OF BIOCHEMISTRY AND BIOPHYSICS, 1973, 155 (01) :213-220
[4]   ENZYMATIC DEFECT IN FABRYS DISEASE - CERAMIDETRIHEXOSIDASE DEFICIENCY [J].
BRADY, RO ;
GAL, AE ;
BRADLEY, RM ;
MARTENSS.E ;
WARSHAW, AL ;
LASTER, L .
NEW ENGLAND JOURNAL OF MEDICINE, 1967, 276 (21) :1163-&
[5]  
CHRISTENSEN LHO, 1966, ACTA PATHOL MIC SC, V68, P332
[6]  
CRAWHALL JC, 1972, SCIENCE, V177, P527, DOI 10.1126/science.177.4048.527
[7]   IDENTIFICATION OF ALPHA-GALACTOSIDASE-B FROM HUMAN LIVER AS AN ALPHA-N-ACETYLGALACTOSAMINIDASE [J].
DEAN, KJ ;
SUNG, SSJ ;
SWEELEY, CC .
BIOCHEMICAL AND BIOPHYSICAL RESEARCH COMMUNICATIONS, 1977, 77 (04) :1411-1417
[8]  
DEAN KJ, 1977, PRACTICAL ENZYMOLOGY, P173
[9]  
DESNICK RJ, 1973, J LAB CLIN MED, V81, P157
[10]  
DESNICK RJ, 1978, METABOLIC BASIS INHE, P810