THE INBORN-ERRORS OF MITOCHONDRIAL FATTY-ACID OXIDATION

[1] THE MULTIPLE ACYL-COENZYME A DEHYDROGENATION DISORDERS, GLUTARIC ACIDURIA TYPE-II AND ETHYLMALONIC-ADIPIC ACIDURIA - MITOCHONDRIAL FATTY-ACID OXIDATION, ACYL-COENZYME-A DEHYDROGENASE, AND ELECTRON-TRANSFER FLAVOPROTEIN ACTIVITIES IN FIBROBLASTS [J]. JOURNAL OF CLINICAL INVESTIGATION, 1986, 78 (01) : 205 - 213

[2] PEROXISOMAL AND MITOCHONDRIAL PALMITOYL COENZYME-A BETA-OXIDATION ACTIVITIES IN RAT WHITE ADIPOSE-TISSUE AND THEIR REGULATION IN HYPOTHYROIDISM [J]. ARCHIVES OF BIOCHEMISTRY AND BIOPHYSICS, 1983, 222 (02) : 416 - 423

[3] REACTION OF ELECTRON-TRANSFER FLAVOPROTEIN WITH ELECTRON-TRANSFER FLAVOPROTEIN-UBIQUINONE OXIDOREDUCTASE [J]. BIOCHEMISTRY, 1985, 24 (15) : 3922 - 3925

[4] GLUTARIC ACIDURIA TYPE-II - BIOCHEMICAL INVESTIGATION AND TREATMENT OF A CHILD DIAGNOSED PRENATALLY [J]. JOURNAL OF INHERITED METABOLIC DISEASE, 1984, 7 (02) : 57 - 61

[5] THE DIAGNOSIS AND BIOCHEMICAL INVESTIGATION OF A PATIENT WITH A SHORT CHAIN FATTY-ACID OXIDATION DEFECT [J]. JOURNAL OF INHERITED METABOLIC DISEASE, 1985, 8 : 135 - 136

[6] BENNETT MJ, 1985, 23RD SSIEM ANN S LIV

[7] ROLE OF ALCOHOL-DEHYDROGENASE IN OMEGA-OXIDATION OF FATTY-ACIDS [J]. EUROPEAN JOURNAL OF BIOCHEMISTRY, 1972, 30 (03): : 441 - &

[8] MICROSOMAL DEHYDROGENATION OF OMEGA1-HYDROXY AND OMEGA2-HYDROXY FATTY-ACIDS [J]. BIOCHIMICA ET BIOPHYSICA ACTA, 1972, 260 (02) : 178 - &

[9] MULTIPLE ACYL-COA DEHYDROGENATION DEFICIENCY (GLUTARIC ACIDURIA TYPE-II), CONGENITAL POLYCYSTIC KIDNEYS, AND SYMMETRIC WARTY DYSPLASIA OF THE CEREBRAL-CORTEX IN 2 NEWBORN BROTHERS .2. MORPHOLOGY AND PATHOGENESIS [J]. EUROPEAN JOURNAL OF PEDIATRICS, 1982, 139 (01) : 60 - 65

[10] MEDIUM-CHAIN ACYL-COA DEHYDROGENASE-DEFICIENCY IN 2 SIBLINGS WITH A REYE-LIKE SYNDROME [J]. JOURNAL OF PEDIATRICS, 1985, 106 (06) : 918 - 921

[1] THE MULTIPLE ACYL-COENZYME A DEHYDROGENATION DISORDERS, GLUTARIC ACIDURIA TYPE-II AND ETHYLMALONIC-ADIPIC ACIDURIA - MITOCHONDRIAL FATTY-ACID OXIDATION, ACYL-COENZYME-A DEHYDROGENASE, AND ELECTRON-TRANSFER FLAVOPROTEIN ACTIVITIES IN FIBROBLASTS [J]. JOURNAL OF CLINICAL INVESTIGATION, 1986, 78 (01) : 205 - 213

[2] PEROXISOMAL AND MITOCHONDRIAL PALMITOYL COENZYME-A BETA-OXIDATION ACTIVITIES IN RAT WHITE ADIPOSE-TISSUE AND THEIR REGULATION IN HYPOTHYROIDISM [J]. ARCHIVES OF BIOCHEMISTRY AND BIOPHYSICS, 1983, 222 (02) : 416 - 423

[3] REACTION OF ELECTRON-TRANSFER FLAVOPROTEIN WITH ELECTRON-TRANSFER FLAVOPROTEIN-UBIQUINONE OXIDOREDUCTASE [J]. BIOCHEMISTRY, 1985, 24 (15) : 3922 - 3925

[4] GLUTARIC ACIDURIA TYPE-II - BIOCHEMICAL INVESTIGATION AND TREATMENT OF A CHILD DIAGNOSED PRENATALLY [J]. JOURNAL OF INHERITED METABOLIC DISEASE, 1984, 7 (02) : 57 - 61

[5] THE DIAGNOSIS AND BIOCHEMICAL INVESTIGATION OF A PATIENT WITH A SHORT CHAIN FATTY-ACID OXIDATION DEFECT [J]. JOURNAL OF INHERITED METABOLIC DISEASE, 1985, 8 : 135 - 136

[6] BENNETT MJ, 1985, 23RD SSIEM ANN S LIV

[7] ROLE OF ALCOHOL-DEHYDROGENASE IN OMEGA-OXIDATION OF FATTY-ACIDS [J]. EUROPEAN JOURNAL OF BIOCHEMISTRY, 1972, 30 (03): : 441 - &

[8] MICROSOMAL DEHYDROGENATION OF OMEGA1-HYDROXY AND OMEGA2-HYDROXY FATTY-ACIDS [J]. BIOCHIMICA ET BIOPHYSICA ACTA, 1972, 260 (02) : 178 - &

[9] MULTIPLE ACYL-COA DEHYDROGENATION DEFICIENCY (GLUTARIC ACIDURIA TYPE-II), CONGENITAL POLYCYSTIC KIDNEYS, AND SYMMETRIC WARTY DYSPLASIA OF THE CEREBRAL-CORTEX IN 2 NEWBORN BROTHERS .2. MORPHOLOGY AND PATHOGENESIS [J]. EUROPEAN JOURNAL OF PEDIATRICS, 1982, 139 (01) : 60 - 65

[10] MEDIUM-CHAIN ACYL-COA DEHYDROGENASE-DEFICIENCY IN 2 SIBLINGS WITH A REYE-LIKE SYNDROME [J]. JOURNAL OF PEDIATRICS, 1985, 106 (06) : 918 - 921