ALPHA-1-ANTITRYPSIN DEFICIENCY - A DEFECT IN SECRETION

被引:7
作者
FOREMAN, RC
机构
关键词
D O I
10.1007/BF01121452
中图分类号
Q5 [生物化学]; Q7 [分子生物学];
学科分类号
071010 ; 081704 ;
摘要
引用
收藏
页码:307 / 311
页数:5
相关论文
共 32 条
[1]   SYNTHESIS AND INSERTION OF CYTOCHROME-P-450 INTO ENDOPLASMIC-RETICULUM MEMBRANES [J].
BARNUN, S ;
KREIBICH, G ;
ADESNIK, M ;
ALTERMAN, L ;
NEGISHI, M ;
SABATINI, DD .
PROCEEDINGS OF THE NATIONAL ACADEMY OF SCIENCES OF THE UNITED STATES OF AMERICA-BIOLOGICAL SCIENCES, 1980, 77 (02) :965-969
[2]   HUMAN Z-ALPHA-1-ANTITRYPSIN ACCUMULATES INTRACELLULARLY AND STIMULATES LYSOSOMAL ACTIVITY WHEN SYNTHESIZED IN THE XENOPUS OOCYTE [J].
BATHURST, IC ;
ERRINGTON, DM ;
FOREMAN, RC ;
JUDAH, JD ;
CARRELL, RW .
FEBS LETTERS, 1985, 183 (02) :304-308
[3]   TRANSLATION AND PROCESSING OF NORMAL (PIMM) AND ABNORMAL (PIZZ) HUMAN ALPHA-1-ANTITRYPSIN [J].
BATHURST, IC ;
STENFLO, J ;
ERRINGTON, DM ;
CARRELL, RW .
FEBS LETTERS, 1983, 153 (02) :270-274
[4]   STRUCTURAL AND FUNCTIONAL-CHARACTERIZATION OF THE ABNORMAL Z-ALPHA1-ANTITRYPSIN ISOLATED FROM HUMAN-LIVER [J].
BATHURST, IC ;
TRAVIS, J ;
GEORGE, PM ;
CARRELL, RW .
FEBS LETTERS, 1984, 177 (02) :179-183
[5]   INTRACELLULAR PROTEIN TOPOGENESIS [J].
BLOBEL, G .
PROCEEDINGS OF THE NATIONAL ACADEMY OF SCIENCES OF THE UNITED STATES OF AMERICA-BIOLOGICAL SCIENCES, 1980, 77 (03) :1496-1500
[6]   TRANSFER OF PROTEINS ACROSS MEMBRANES .2. RECONSTITUTION OF FUNCTIONAL ROUGH MICROSOMES FROM HETEROLOGOUS COMPONENTS [J].
BLOBEL, G ;
DOBBERSTEIN, B .
JOURNAL OF CELL BIOLOGY, 1975, 67 (03) :852-862
[7]  
Blobel G., 1971, BIOMEMBRANE, V2, P193
[8]  
CARRELL RW, 1979, ESSAYS MEDICAL BIOCH, V4, P83
[9]  
Colman A., 1984, TRANSCRIPTION TRANSL
[10]   SYNTHESIS IN ESCHERICHIA-COLI OF ALPHA-1-ANTITRYPSIN VARIANTS OF THERAPEUTIC POTENTIAL FOR EMPHYSEMA AND THROMBOSIS [J].
COURTNEY, M ;
JALLAT, S ;
TESSIER, LH ;
BENAVENTE, A ;
CRYSTAL, RG ;
LECOCQ, JP .
NATURE, 1985, 313 (5998) :149-151