DELAY TIME OF HEMOGLOBIN-S POLYMERIZATION PREVENTS MOST CELLS FROM SICKLING INVIVO

被引:168
作者
MOZZARELLI, A
HOFRICHTER, J
EATON, WA
机构
[1] NIDDKD,CHEM PHYS LAB,BETHESDA,MD 20205
[2] NIH,BETHESDA,MD 20892
关键词
D O I
10.1126/science.3603036
中图分类号
O [数理科学和化学]; P [天文学、地球科学]; Q [生物科学]; N [自然科学总论];
学科分类号
07 ; 0710 ; 09 ;
摘要
引用
收藏
页码:500 / 506
页数:7
相关论文
共 48 条
[1]  
Altman P. L., 1971, RESPIRATION CIRCULAT
[2]  
BOOKCHIN RM, 1976, J LAB CLIN MED, V87, P597
[3]   CARBON-MONOXIDE BINDING BY HEMOGLOBIN AND MYOGLOBIN UNDER PHOTODISSOCIATING CONDITIONS [J].
BRUNORI, M ;
ANTONINI, E ;
BONAVENT.C ;
BONAVENT.J ;
WYMAN, J .
PROCEEDINGS OF THE NATIONAL ACADEMY OF SCIENCES OF THE UNITED STATES OF AMERICA, 1972, 69 (04) :868-&
[4]  
Bunn HF., 1986, HEMOGLOBIN MOL GENET
[5]   KINETICS OF SICKLE HEMOGLOBIN POLYMERIZATION IN SINGLE RED-CELLS [J].
COLETTA, M ;
HOFRICHTER, J ;
FERRONE, FA ;
EATON, WA .
NATURE, 1982, 300 (5888) :194-197
[6]  
Eaton W A, 1981, Methods Enzymol, V76, P175
[7]  
EATON WA, 1976, BLOOD, V47, P621
[8]  
EATON WA, IN PRESS BLOOD
[9]   MOLECULAR TOPOLOGY IN CRYSTALS AND FIBERS OF HEMOGLOBIN-S [J].
EDELSTEIN, SJ .
JOURNAL OF MOLECULAR BIOLOGY, 1981, 150 (04) :557-575
[10]  
FABRY ME, 1984, BLOOD, V64, P1042