ABSENCE OF MALIGNANT HYPERTHERMIA CONTRACTURES IN BECKER-DUCHENNE DYSTROPHY AT AGE-2

被引:14
作者
GRONERT, GA
FOWLER, W
CARDINET, GH
GRIX, A
ELLIS, WG
SCHWARTZ, MZ
机构
[1] UNIV CALIF DAVIS,DEPT PHYS MED & REHABIL,DAVIS,CA 95616
[2] UNIV CALIF DAVIS,DEPT VET ANAT,DAVIS,CA 95616
[3] UNIV CALIF DAVIS,DEPT PEDIAT & GENET,DAVIS,CA 95616
[4] UNIV CALIF DAVIS,DEPT PATHOL,DAVIS,CA 95616
[5] UNIV CALIF DAVIS,DEPT PEDIAT,DAVIS,CA 95616
[6] UNIV CALIF DAVIS,DEPT SURG,DAVIS,CA 95616
关键词
BECKER DYSTROPHY; DUCHENNE MUSCULAR DYSTROPHY; MALIGNANT HYPERTHERMIA; MYOPATHY; HYPERTHERMIA; MALIGNANT; HALOTHANE CONTRACTURES; CAFFEINE CONTRACTURES;
D O I
10.1002/mus.880150110
中图分类号
R74 [神经病学与精神病学];
学科分类号
摘要
Two 2-year-old males underwent muscle biopsy that established the histopathologic diagnosis of Becker dystrophy in one, and Duchenne dystrophy in the other. Concomitant contracture testing with caffeine or halothane was normal for malignant hyperthermia (MH). The results suggest that acute hypermetabolism or acute rhabdomyolysis during anesthesia, in patients with these disorders, is related to the X-linked myopathy and its associated muscle deterioration, rather than to the autosomal dominant MH.
引用
收藏
页码:52 / 56
页数:5
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