DIAGNOSIS AND TREATMENT OF HOMOZYGOUS PROTEIN-C DEFICIENCY

被引:203
作者
MARLAR, RA
MONTGOMERY, RR
BROEKMANS, AW
机构
[1] UNIV COLORADO, HLTH SCI CTR, DEPT BIOCHEM, DENVER, CO 80262 USA
[2] UNIV COLORADO, HLTH SCI CTR, DEPT GENET, DENVER, CO 80262 USA
[3] VET ADM MED CTR, DENVER, CO 80220 USA
[4] BLOOD CTR SE WISCONSIN, MILWAUKEE, WI USA
[5] STATE UNIV LEIDEN HOSP, HEMOSTASIS & THROMBOSIS RES UNIT, 2333 AA LEIDEN, NETHERLANDS
关键词
D O I
10.1016/S0022-3476(89)80688-2
中图分类号
R72 [儿科学];
学科分类号
100202 ;
摘要
引用
收藏
页码:528 / 534
页数:7
相关论文
共 31 条
[1]  
ALLEN DM, 1966, PEDIATRICS, V38, P211
[2]   DEVELOPMENT OF THE HUMAN COAGULATION SYSTEM IN THE FULL-TERM INFANT [J].
ANDREW, M ;
PAES, B ;
MILNER, R ;
JOHNSTON, M ;
MITCHELL, L ;
TOLLEFSEN, DM ;
POWERS, P .
BLOOD, 1987, 70 (01) :165-172
[3]  
BERTINA RM, 1984, THROMB HAEMOSTASIS, V51, P1
[4]  
BRANSON HE, 1983, LANCET, V2, P1165
[5]   CONGENITAL PROTEIN-C DEFICIENCY AND VENOUS THROMBOEMBOLISM - A STUDY OF 3 DUTCH FAMILIES [J].
BROEKMANS, AW ;
VELTKAMP, JJ ;
BERTINA, RM .
NEW ENGLAND JOURNAL OF MEDICINE, 1983, 309 (06) :340-344
[6]  
BROEKMANS AW, 1983, THROMB HAEMOSTASIS, V50, P350
[7]   THE REGULATION OF HEMOSTASIS - THE PROTEIN-C SYSTEM [J].
CLOUSE, LH ;
COMP, PC .
NEW ENGLAND JOURNAL OF MEDICINE, 1986, 314 (20) :1298-1304
[8]  
ESTELLES A, 1984, THROMB HAEMOSTASIS, V52, P53
[9]  
GARCIAPLAZA I, 1985, LANCET, V1, P634
[10]   DEFICIENCY OF PROTEIN-C IN CONGENITAL THROMBOTIC DISEASE [J].
GRIFFIN, JH ;
EVATT, B ;
ZIMMERMAN, TS ;
KLEISS, AJ ;
WIDEMAN, C .
JOURNAL OF CLINICAL INVESTIGATION, 1981, 68 (05) :1370-1373