ACCUMULATION OF GLYCOLIPIDS CONTAINING N-ACETYLGLUCOSAMINE IN ERYTHROCYTE STROMA OF PATIENTS WITH CONGENITAL DYSERYTHROPOIETIC ANEMIA TYPE-2 (HEMPAS)

被引:21
作者
JOSEPH, KC
GOCKERMAN, JP
机构
[1] NIAMDD,BETHESDA,MD 20014
[2] UNIV KENTUCKY,MED CTR,DEPT HEMATOL,LEXINGTON,KY 40506
关键词
D O I
10.1016/S0006-291X(75)80072-6
中图分类号
Q5 [生物化学]; Q7 [分子生物学];
学科分类号
071010 ; 081704 ;
摘要
引用
收藏
页码:146 / 152
页数:7
相关论文
共 21 条
[1]   ISOLATION OF MUCIC ACID FROM FRUITS [J].
ANET, EFLJ ;
REYNOLDS, TM .
NATURE, 1954, 174 (4437) :930-930
[2]   ENZYMATIC DEFECT IN FABRYS DISEASE - CERAMIDETRIHEXOSIDASE DEFICIENCY [J].
BRADY, RO ;
GAL, AE ;
BRADLEY, RM ;
MARTENSS.E ;
WARSHAW, AL ;
LASTER, L .
NEW ENGLAND JOURNAL OF MEDICINE, 1967, 276 (21) :1163-&
[3]  
CARTER HE, 1967, J LIPID RES, V8, P391
[4]  
ESSELMAN WJ, 1972, METHOD ENZYMOL, V28, P140
[5]  
FITZGERALD DK, 1970, J BIOL CHEM, V245, P2103
[6]  
Frederickson DS, 1972, METABOLIC BASIS INHE, P730
[7]  
HAKOMORI SI, 1964, J BIOCHEM-TOKYO, V55, P205
[8]  
JOSEPH KC, 1975, J LAB CLIN MED, V85, P34
[9]  
KOBATA A, 1972, METHOD ENZYMOL, V28, P262
[10]  
LI Y, 1972, METHODS ENZYMOL, V20, P714