METHOD FOR ALPHA-L-IDURONIDASE ASSAY

被引:20
作者
SINGH, J
NIEBES, P
DIFERRAN.N
机构
[1] BAYLOR UNIV, COLL MED, MARRS MCLEAN DEPT BIOCHEM, LABS CONNECT TISSUE RES, HOUSTON, TX 77025 USA
[2] BAYLOR UNIV, COLL MED, DEPT MED, HOUSTON, TX 77025 USA
[3] ZYMA SA, NYON, SWITZERLAND
[4] BAYLOR UNIV, COLL MED, DEPT SURG, DIV ORTHOPEDIC SURG, HOUSTON, TX 77025 USA
来源
FEBS LETTERS | 1974年 / 45卷 / 01期
关键词
D O I
10.1016/0014-5793(74)80854-9
中图分类号
Q5 [生物化学]; Q7 [分子生物学];
学科分类号
071010 ; 081704 ;
摘要
引用
收藏
页码:248 / 251
页数:4
相关论文
共 11 条
[1]   DEFECT IN HURLER AND SCHEIE SYNDROMES - DEFICIENCY OF ALPHA-IDURONIDASE [J].
BACH, G ;
WEISSMAN.B ;
FRIEDMAN, R ;
NEUFELD, EF .
PROCEEDINGS OF THE NATIONAL ACADEMY OF SCIENCES OF THE UNITED STATES OF AMERICA, 1972, 69 (08) :2048-&
[2]  
BEAUDET AL, TO BE PUBLISHED
[3]  
BERATIS NG, 1973, J PEDIATR-US, V83, P824, DOI 10.1016/S0022-3476(73)80377-4
[4]   PHENYL ALPHA-L-IDOPYRANOSIDURONIC AND BETA-L-IDOPYRANOSIDURONIC ACIDS AND SOME OTHER ARYL GLYCOPYRANOSIDURONIC ACIDS [J].
FRIEDMAN, RB ;
WEISSMANN, B .
CARBOHYDRATE RESEARCH, 1972, 24 (01) :123-+
[5]  
GLASER JH, 1973, J LAB CLIN MED, V82, P969
[6]   ALPHA-L-IDURONIDASE ACTIVITY IN CULTURED SKIN FIBROBLASTS AND AMNIOTIC-FLUID CELLS [J].
HALL, CW ;
NEUFELD, EF .
ARCHIVES OF BIOCHEMISTRY AND BIOPHYSICS, 1973, 158 (02) :817-821
[7]  
LOWRY OH, 1951, J BIOL CHEM, V193, P265
[8]   L-IDURONIDASE IN CULTURED HUMAN FIBROBLASTS AND LIVER [J].
MATALON, R ;
CIFONELLI, JA ;
DORFMAN, A .
BIOCHEMICAL AND BIOPHYSICAL RESEARCH COMMUNICATIONS, 1971, 42 (02) :340-+
[9]  
NOLLER CR, 1957, CHEMISTRY ORGANIC CO
[10]   ALPHA-L-DIURONIDASE IN LYSOSOMAL EXTRACTS [J].
WEISSMANN, B ;
SANTIAGO, R .
BIOCHEMICAL AND BIOPHYSICAL RESEARCH COMMUNICATIONS, 1972, 46 (03) :1430-+