BULBO-PONTINE PARALYSIS WITH DEAFNESS - THE VIALETTO-VANLAERE SYNDROME

被引：16

作者：

ABARBANEL, JM

ASHBY, P

MARQUEZJULIO, A

CHAPMAN, KR

机构：

[1] TORONTO HOSP, DEPT ELECTROMYOG, 399 BATHURST ST, TORONTO M5T 2S8, ONTARIO, CANADA

[2] BEN GURION UNIV NEGEV, FAC HLTH SCI, SOROKA MED CTR, DEPT NEUROL, BEER SHEVA, ISRAEL

来源：

CANADIAN JOURNAL OF NEUROLOGICAL SCIENCES | 1991年 / 18卷 / 03期

关键词：

D O I：

10.1017/S0317167100031930

中图分类号：

R74 [神经病学与精神病学];

学科分类号：

摘要：

A Caucasian girl developed slowly progressive sensory neural deafness and bulbar and spinal muscle weakness typical of the Vialetto-Van Laere syndrome. As the condition progressed the major disabilities became dysphagia, respiratory muscle weakness and postural hypotension. Treatment with gastrostomy feedings, oxygen and fluorocortisone acetate produced worthwhile functional improvement.

引用

页码：349 / 351

页数：3

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