NON-INVASIVE EVALUATION OF VENTRICULAR-FUNCTION IN CYSTIC-FIBROSIS

被引:48
作者
CHIPPS, BE
ALDERSON, PO
ROLAND, JMA
YANG, S
VANASWEGEN, A
MARTINEZ, CR
ROSENSTEIN, BJ
机构
[1] JOHNS HOPKINS MED INST, DEPT PEDIAT, BALTIMORE, MD 21205 USA
[2] JOHNS HOPKINS MED INST, DEPT RADIOL, BALTIMORE, MD 21205 USA
关键词
D O I
10.1016/S0022-3476(79)80510-7
中图分类号
R72 [儿科学];
学科分类号
100202 ;
摘要
The cardiac function of 21 patients with cystic fibrosis was studied using radionuclides and M-mode echocardiography. The patients (mean age 13.2 years, range 4 to 27) had a wide range of clinical and pulmonary function abnormalities (mean Shwachman-Kulczycki score 62.1). Decreased right ventricular ejection fraction was found in 13 of 18 patients (72%); an additional four patients had abnormal septal motion on ECHO. Left ventricular ejection fraction was abnormal at rest in four patients (19%); an additional four patients had borderline low LVEF. The LV pre-ejection period to ejection time ratio increased significantly (i.e., worsening LV performance) with deterioration of S-K score, chest radiograph score, and forced expiratory volume in 1 second. Three of eight patients with normal LVEF at rest had an abnormal response to supine bicycle exercise: LVEF fell in two patients and was unchanged in one. Thus evidence of LV dysfunction was observed in seven of 21 (33%) of the patients; four at rest and in three only during exercise. © 1979 The C. V. Mosby Company.
引用
收藏
页码:379 / 384
页数:6
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