EVALUATION AND MANAGEMENT OF CARNEYS COMPLEX - AN ILLUSTRATIVE CASE

被引：7

作者：

WALLACE, TM ^{[1
]}

LEVIN, HS ^{[1
]}

RATLIFF, NB ^{[1
]}

HOBBS, RE ^{[1
]}

机构：

[1] CLEVELAND CLIN FDN,CTR CLIN 1,DEPT PATHOL,9500 EUCLID AVE,CLEVELAND,OH 44195

来源：

CLEVELAND CLINIC JOURNAL OF MEDICINE | 1991年 / 58卷 / 03期

关键词：

CARNEYS COMPLEX;

D O I：

10.3949/ccjm.58.3.248

中图分类号：

R5 [内科学];

学科分类号：

1002 ; 100201 ;

摘要：

Carney's complex is characterized by cardiac and cutaneous myxomas, mammary myxoid fibroadenomas, spotty mucocutaneous pigmentation, primary pigmented adrenocortical disease, large-cell calcifying Sertoli cell tumors of the testis, growth hormone-secreting pituitary adenomas, and psammomatous melanotic schwannomas. We present an illustrative case of Carney's complex in a 26-year-old woman who at age 20 underwent bilateral adrenalectomy for Cushing's syndrome. Six years later, she suffered multiple central nervous system embolic episodes secondary to three cardiac myxomas, which led to her death. Appropriate evaluation and management of patients with Carney's complex is outlined.

引用

页码：248 / 256

页数：9