GLANZMANN THROMBASTHENIA - DEFICIENT BINDING OF VONWILLEBRAND-FACTOR TO THROMBIN-STIMULATED PLATELETS

被引:253
作者
RUGGERI, ZM
BADER, R
DEMARCO, L
机构
[1] SCRIPPS CLIN & RES FDN,DEPT BASIC & CLIN RES,LA JOLLA,CA 92037
[2] OSPED CIVILE,CTR TRASFUS,PORDENONE,ITALY
来源
PROCEEDINGS OF THE NATIONAL ACADEMY OF SCIENCES OF THE UNITED STATES OF AMERICA-BIOLOGICAL SCIENCES | 1982年 / 79卷 / 19期
关键词
D O I
10.1073/pnas.79.19.6038
中图分类号
Q [生物科学];
学科分类号
07 ; 0710 ; 09 ;
摘要
引用
收藏
页码:6038 / 6041
页数:4
相关论文
共 31 条
[1]   EXPOSURE OF PLATELET FIBRINOGEN RECEPTORS BY ADP AND EPINEPHRINE [J].
BENNETT, JS ;
VILAIRE, G .
JOURNAL OF CLINICAL INVESTIGATION, 1979, 64 (05) :1393-1401
[2]  
CAEN J, 1972, CLIN HAEMATOL, V1, P383
[3]   ADDITIONAL PLATELET MEMBRANE GLYCOPROTEIN ABNORMALITIES IN GLANZMANNS THROMBASTHENIA - A COMPARISON WITH NORMALS BY HIGH-RESOLUTION TWO-DIMENSIONAL POLYACRYLAMIDE-GEL ELECTROPHORESIS [J].
CLEMETSON, KJ ;
CAPITANIO, A ;
PARETI, FI ;
MCGREGOR, JL ;
LUSCHER, EF .
THROMBOSIS RESEARCH, 1980, 18 (06) :797-806
[4]   PROPERTIES OF HUMAN ASIALO-FACTOR-VIII - A RISTOCETIN-INDEPENDENT PLATELET-AGGREGATING AGENT [J].
DEMARCO, L ;
SHAPIRO, SS .
JOURNAL OF CLINICAL INVESTIGATION, 1981, 68 (02) :321-328
[5]  
FRAKER PJ, 1978, BIOCHEM BIOPH RES CO, V80, P849, DOI 10.1016/0006-291X(78)91322-0
[6]   THROMBIN-INDUCED EXPOSURE AND PROSTACYCLIN INHIBITION OF THE RECEPTOR FOR FACTOR-VIII/VONWILLEBRAND FACTOR ON HUMAN-PLATELETS [J].
FUJIMOTO, T ;
OHARA, S ;
HAWIGER, J .
JOURNAL OF CLINICAL INVESTIGATION, 1982, 69 (06) :1212-1222
[7]  
GERRARD JM, 1979, AM J PATHOL, V94, P509
[8]  
GINSBERG M, 1981, THROMB HAEMOSTASIS, V46, P84
[9]   PLATELET-ADHESIVENESS AND AGGREGATION IN CONGENITAL AFIBRINOGENEMIA - INVESTIGATION OF 3 PATIENTS WITH POST-TRANSFUSION, CROSS-CORRECTION STUDIES BETWEEN 2 OF THEM [J].
GIROLAMI, A ;
DEMARCO, L ;
VIRGOLINI, L ;
PERUFFO, R ;
FABRIS, F .
BLUT, 1975, 30 (02) :87-100
[10]   PROSTACYCLIN INHIBITS MOBILIZATION OF FIBRINOGEN-BINDING SITES ON HUMAN ADP-TREATED AND THROMBIN-TREATED PLATELETS [J].
HAWIGER, J ;
PARKINSON, S ;
TIMMONS, S .
NATURE, 1980, 283 (5743) :195-197