GLYCOGENOSIS TYPE-IV - LIVER-TRANSPLANT AT 12 YEARS

被引：10

作者：

DHAWAN, A

TAN, KC

PORTMANN, B

MOWAT, AP

机构：

[1] UNIV LONDON KINGS COLL HOSP,DEPT CHILD HLTH,LONDON SE5 8RX,ENGLAND

[2] UNIV LONDON KINGS COLL HOSP,INST LIVER STUDIES,LONDON SE5 8RX,ENGLAND

来源：

ARCHIVES OF DISEASE IN CHILDHOOD | 1994年 / 71卷 / 05期

关键词：

D O I：

10.1136/adc.71.5.450

中图分类号：

R72 [儿科学];

学科分类号：

100202 ;

摘要：

Hepatomegaly, the presenting feature of type IV glycogen storage disease at 20 months of age, regressed during childhood. The patient remained asymptomatic until 12 years of age when, after an episode of shock, septicaemia, and spontaneous peritonitis, liver transplantation was successfully performed.

引用

页码：450 / 451

页数：2

共 6 条

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STARZL, TE
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