PERIOPERATIVE MANAGEMENT OF PATIENTS WITH VONWILLEBRANDS DISEASE

被引:10
作者
CAMERON, CB [1 ]
KOBRINSKY, N [1 ]
机构
[1] UNIV MANITOBA,CHILDRENS HOSP,DEPT PAEDIAT,WINNIPEG R3A 1S1,MANITOBA,CANADA
来源
CANADIAN JOURNAL OF ANAESTHESIA-JOURNAL CANADIEN D ANESTHESIE | 1990年 / 37卷 / 03期
关键词
blood:; coagulation; haemorrhage; replacement;
D O I
10.1007/BF03005587
中图分类号
R614 [麻醉学];
学科分类号
100217 ;
摘要
This review focuses on the pathophysiology of the Factor VIII molecule as it relates to Von Willebrand's disease. Three major categories of Von Willebrand' s disease are identified. The perioperative diagnosis and management of all categories are reviewed. 1-Deamino-8-D-argnine vasopressin (DDAVP) is presented as an alternative to the transfusion of blood and blood products for the management of a bleeding diathesis. © 1990 Canadian Anesthesiologists.
引用
收藏
页码:341 / 347
页数:7
相关论文
共 30 条
[1]  
[Anonymous], 1926, FIN LAKARESALLSK HAN
[3]   FACTOR-VIII RECOMBINATION AFTER DISSOCIATION BY CACL2 [J].
COOPER, HA ;
GRIGGS, TR ;
WAGNER, RH .
PROCEEDINGS OF THE NATIONAL ACADEMY OF SCIENCES OF THE UNITED STATES OF AMERICA, 1973, 70 (08) :2326-2329
[4]   TRANSFUSION STUDIES IN VON WILLEBRANDS DISEASES - EFFECT ON BLEEDING TIME AND FACTOR VIII [J].
CORNU, P ;
CAEN, J ;
BERNARD, J ;
LARRIEU, MJ .
BRITISH JOURNAL OF HAEMATOLOGY, 1963, 9 (02) :189-&
[5]  
DEMARCO L, 1982, BLOOD S1, V60, pA198
[6]   PURIFICATION AND CHARACTERIZATION OF A HIGHLY PURIFIED HUMAN FACTOR-VIII CONSISTING OF A SINGLE TYPE OF POLYPEPTIDE-CHAIN [J].
FAY, PJ ;
CHAVIN, SI ;
SCHROEDER, D ;
YOUNG, FE ;
MARDER, VJ .
PROCEEDINGS OF THE NATIONAL ACADEMY OF SCIENCES OF THE UNITED STATES OF AMERICA-BIOLOGICAL SCIENCES, 1982, 79 (23) :7200-7204
[7]   CHARACTERIZATION OF THE HUMAN FACTOR-VIII PROCOAGULANT PROTEIN WITH A HETEROLOGOUS PRECIPITATING ANTIBODY [J].
FULCHER, CA ;
ZIMMERMAN, TS .
PROCEEDINGS OF THE NATIONAL ACADEMY OF SCIENCES OF THE UNITED STATES OF AMERICA-BIOLOGICAL SCIENCES, 1982, 79 (05) :1648-1652
[8]   FACTOR-VIII [J].
GRALNICK, HR ;
COLLER, BS ;
SHULMAN, NR ;
ANDERSEN, JC ;
HILGARTNER, M .
ANNALS OF INTERNAL MEDICINE, 1977, 86 (05) :598-616
[9]   FAILURE OF AHF CONCENTRATE TO CONTROL BLEEDING IN VONWILLEBRANDS DISEASE [J].
GREEN, D ;
POTTER, EV .
AMERICAN JOURNAL OF MEDICINE, 1976, 60 (03) :357-360
[10]  
Hoyer L W, 1976, Prog Hemost Thromb, V3, P231