HEMISPHERIC DISCONNECTION IN MARCHIAFAVA-BIGNAMI DISEASE - CLINICAL, NEUROPSYCHOLOGICAL AND MRI FINDINGS

被引:35
作者
BEREK, K [1 ]
WAGNER, M [1 ]
CHEMELLI, AP [1 ]
AICHNER, F [1 ]
BENKE, T [1 ]
机构
[1] UNIV INNSBRUCK HOSP,DEPT MAGNET RESONANCE,A-6020 INNSBRUCK,AUSTRIA
关键词
MARCHIAFAVA-BIGNAMI DISEASE; CALLOSAL NECROSIS; HEMISPHERIC DISCONNECTION SYNDROME;
D O I
10.1016/0022-510X(94)90195-3
中图分类号
R74 [神经病学与精神病学];
学科分类号
摘要
We report a single-case study of a patient suffering from Marchiafava-Bignami disease (MBD), a rarely intra vitam diagnosed syndrome with focal demyelination in the corpus callosum, which is usually found in patients with chronic alcohol abuse. Our study explored a variety of motor, sensory and visual functions. Striking features were left apraxia caused by two lesions in the rostral area, and left hemidyslexia related to a large splenial lesion demonstrated by MRI. As symptoms of disconnection may remain undetected clinically, MRI is a most useful tool for the diagnosis of MBD.
引用
收藏
页码:2 / 5
页数:4
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