IDIOPATHIC INFANTILE ARTERIAL CALCIFICATION IN SIBLINGS - RADIOLOGIC-DIAGNOSIS AND SUCCESSFUL TREATMENT

被引:81
作者
MERADJI, M
DEVILLENEUVE, VH
HUBER, J
DEBRUIJN, WC
PEARSE, RG
机构
[1] ERASMUS UNIV, SOPHIA CHILDRENS HOSP, NEONATAL UNIT, ROTTERDAM, NETHERLANDS
[2] ERASMUS UNIV, SOPHIA CHILDRENS HOSP, DEPT CLIN PATHOL, ROTTERDAM, NETHERLANDS
[3] ERASMUS UNIV, SOPHIA CHILDRENS HOSP, DEPT PEDIAT, ROTTERDAM, NETHERLANDS
关键词
D O I
10.1016/S0022-3476(78)80427-2
中图分类号
R72 [儿科学];
学科分类号
100202 ;
摘要
Idiopathic infantile arterial calcification is a disorder of unknown etiology manifested by widespread arterial calcification. This usually leads to early death from coronary artery occlusion. In 12 of the 75 cases in the literature, radiographs were taken and it was possible to make the diagnosis in them all. We present two patients, siblings, in whom the diagnosis was established radiologically. The nature of the calcium deposits was studied in one of the infants and proved to be calcium hydroxyapatite. Therapy with diphosphonate was apparently successful in the other child. © 1978 The C. V. Mosby Company.
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页码:401 / 405
页数:5
相关论文
共 15 条
  • [1] BACON JF, 1964, JAMA-J AM MED ASSOC, V188, P933
  • [2] BICKEL E, 1963, Arch Kinderheilkd, V169, P274
  • [3] Bryant JH, 1901, GUYS HOSP REP, V55, P17
  • [4] Durante G, 1899, B SOC ANAT PARIS, V74, P97
  • [5] FIELD MH, 1946, ARCH PATHOL, V42, P607
  • [6] IDIOPATHIC INFANTILE ARTERIAL CALCIFICATION - ROENTGEN DIAGNOSIS OF A RARE CAUSE OF CORONARY ARTERY OCCLUSION
    LUSSIERLAZAROFF, J
    FLETCHER, BD
    [J]. PEDIATRIC RADIOLOGY, 1973, 1 (04) : 224 - 228
  • [7] MCKUSICK VA, 1966, HERITABLE DISORDERS
  • [8] MORAN II, 1959, AM J CLIN PATHOL, V31, P517
  • [9] MORAN JJ, 1962, AM J CLIN PATHOL, V37, P521
  • [10] Parker R J, 1971, Clin Radiol, V22, P69