METABOLISM OF H-3 DEHYDROEPIANDROSTERONE SULFATE BY SUBJECTS WITH STEROID SULFATASE DEFICIENCY

被引:15
作者
BERGNER, EA [1 ]
SHAPIRO, LJ [1 ]
机构
[1] UNIV CALIF LOS ANGELES,LOS ANGELES CTY HARBOR MED CTR,SCH MED,DEPT BIOL CHEM,TORRANCE,CA 90502
关键词
D O I
10.1007/BF01800429
中图分类号
R5 [内科学];
学科分类号
1002 ; 100201 ;
摘要
引用
收藏
页码:403 / 415
页数:13
相关论文
共 35 条
[1]   ABSORPTION OF ESTRONE SULFATE FROM THE GASTROINTESTINAL-TRACT OF THE RAT [J].
BACK, DJ ;
CHAPMAN, CR ;
MAY, SA ;
ROWE, PH .
JOURNAL OF STEROID BIOCHEMISTRY AND MOLECULAR BIOLOGY, 1981, 14 (04) :347-356
[2]   SULFATASE ACTIVITY OF KERATINIZING TISSUES IN X-LINKED ICHTHYOSIS [J].
BADEN, HP ;
HOOKER, PA ;
KUBILUS, J ;
TARASCIO, A .
PEDIATRIC RESEARCH, 1980, 14 (12) :1347-1348
[3]   ISOLATION AND CHARACTERIZATION OF A STEROID SULFATASE CDNA CLONE - GENOMIC DELETIONS IN PATIENTS WITH X-CHROMOSOME-LINKED ICHTHYOSIS [J].
BALLABIO, A ;
PARENTI, G ;
CARROZZO, R ;
SEBASTIO, G ;
ANDRIA, G ;
BUCKLE, V ;
FRASER, N ;
CRAIG, I ;
ROCCHI, M ;
ROMEO, G ;
JOBSIS, AC ;
PERSICO, MG .
PROCEEDINGS OF THE NATIONAL ACADEMY OF SCIENCES OF THE UNITED STATES OF AMERICA, 1987, 84 (13) :4519-4523
[4]  
BAULIEU ETIENNE-EMILE, 1965, RECENT PROG HORMONE RES, V21, P411
[5]   INCREASED CHOLESTEROL SULFATE IN PLASMA AND RED-BLOOD-CELL MEMBRANES OF STEROID SULFATASE DEFICIENT PATIENTS [J].
BERGNER, EA ;
SHAPIRO, LJ .
JOURNAL OF CLINICAL ENDOCRINOLOGY & METABOLISM, 1981, 53 (01) :221-223
[6]  
BERNSTEIN S, 1970, CHEM BIOL ASPECTS ST, P1
[7]  
BLEAU G, 1971, CAN J BIOCHEM, V50, P277
[8]   GENETIC-HETEROGENEITY OF STEROID SULFATASE DEFICIENCY REVEALED WITH CDNA FOR HUMAN STEROID SULFATASE [J].
CONARY, JT ;
LORKOWSKI, G ;
SCHMIDT, B ;
POHLMANN, R ;
NAGEL, G ;
MEYER, HE ;
KRENTLER, C ;
CULLY, J ;
HASILIK, A ;
VONFIGURA, K .
BIOCHEMICAL AND BIOPHYSICAL RESEARCH COMMUNICATIONS, 1987, 144 (02) :1010-1017
[9]   HAIR ROOT ANALYSIS IN X-LINKED ICHTHYOSIS [J].
DANCIS, J ;
JANSEN, V ;
HUTZLER, J .
JOURNAL OF INHERITED METABOLIC DISEASE, 1983, 6 (04) :173-177
[10]   UNCONJUGATED DEHYDROEPIANDROSTERONE PLASMA-LEVELS IN NORMAL SUBJECTS FROM BIRTH TO ADOLESCENCE IN HUMAN - USE OF A SENSITIVE RADIOIMMUNOASSAY [J].
DEPERETTI, E ;
FOREST, MG .
JOURNAL OF CLINICAL ENDOCRINOLOGY & METABOLISM, 1976, 43 (05) :982-991