CONGENITAL FASCIAL DYSTROPHY - STIFF SKIN SYNDROME - A HUMAN COUNTERPART OF THE TIGHT-SKIN MOUSE

被引:30
作者
JABLONSKA, S
SCHUBERT, H
KIKUCHI, I
机构
[1] ERFURT SCH MED,DEPT DERMATOL,ERFURT,GER DEM REP
[2] MIYAZAKI MED COLL,KIYATAKE,JAPAN
关键词
D O I
10.1016/S0190-9622(89)70280-2
中图分类号
R75 [皮肤病学与性病学];
学科分类号
100206 ;
摘要
引用
收藏
页码:943 / 950
页数:8
相关论文
共 9 条
[1]  
ESTERLY NB, 1971, PEDIATRICS, V47, P360
[2]   VARIABILITY IN COLLAGEN AND FIBRONECTIN SYNTHESIS BY SCLERODERMA FIBROBLASTS IN PRIMARY CULTURE [J].
FLEISCHMAJER, R ;
PERLISH, JS ;
KRIEG, T ;
TIMPL, R .
JOURNAL OF INVESTIGATIVE DERMATOLOGY, 1981, 76 (05) :400-403
[3]  
GREEN MC, 1976, AM J PATHOL, V82, P493
[4]  
Jablonska S, 1984, Pediatr Dermatol, V2, P87, DOI 10.1111/j.1525-1470.1984.tb00453.x
[5]   SCLERODERMA-LIKE ALTERATIONS IN COLLAGEN-METABOLISM OCCURRING IN THE TSK (TIGHT SKIN) MOUSE [J].
JIMENEZ, SA ;
MILLAN, A ;
BASHEY, RI .
ARTHRITIS AND RHEUMATISM, 1984, 27 (02) :180-185
[6]  
KIKUCHI I, 1987, 4TH P INT C PED DERM, P629
[7]   SCLERODERMA FIBROBLASTS - SOME ASPECTS OF INVITRO ASSESSMENT OF COLLAGEN-SYNTHESIS [J].
KRIEG, T ;
LUDERSCHMIDT, C ;
WEBER, L ;
MULLER, PK ;
BRAUNFALCO, O .
ARCHIVES OF DERMATOLOGICAL RESEARCH, 1981, 270 (03) :263-272
[8]  
KUKUCHI I, 1985, PEDIATR DERMATOL, V3, P48
[9]   STRUCTURE AND TENSILE PROPERTIES OF SKIN OF TIGHT-SKIN (TSK) MUTANT MICE [J].
MENTON, DN ;
HESS, RA ;
LICHTENSTEIN, JR ;
EISEN, AZ .
JOURNAL OF INVESTIGATIVE DERMATOLOGY, 1978, 70 (01) :4-10