DECREASED TRANSPORT OF ORNITHINE ACROSS THE INNER MITOCHONDRIAL-MEMBRANE AS A CAUSE OF HYPERORNITHINEMIA

被引:36
作者
HOMMES, FA
HO, CK
ROESEL, RA
CORYELL, ME
GORDON, BA
机构
[1] MED COLL GEORGIA,DEPT PEDIAT,AUGUSTA,GA 30912
[2] GRACEWOOD STATE SCH & HOSP,GRACEWOOD,GA 30812
[3] CHILDRENS PSYCHIAT RES INST,LONDON,ONTARIO,CANADA
关键词
D O I
10.1007/BF01799753
中图分类号
R5 [内科学];
学科分类号
1002 ; 100201 ;
摘要
引用
收藏
页码:41 / 47
页数:7
相关论文
共 41 条
[1]  
BENSON EL, 1976, BRIT J OPHTHALMOL, V60, P142
[2]   REGULATION OF PYRUVATE OXIDATION IN MITOCHONDRIA ISOLATED FROM FETAL AND ADULT RAT-LIVER [J].
BERGER, R ;
HOMMES, FA .
BIOCHIMICA ET BIOPHYSICA ACTA, 1973, 314 (01) :1-7
[3]  
BICKEL H, 1968, DEUT MED WOCHENSCHR, V47, P2247
[4]   EVIDENCE FOR THE EXISTENCE OF AN ORNITHINE-CITRULLINE ANTIPORTER IN RAT-LIVER MITOCHONDRIA [J].
BRADFORD, NM ;
MCGIVAN, JD .
FEBS LETTERS, 1980, 113 (02) :294-298
[5]   COMPARTMENTALIZED ENZYME DISTRIBUTION IN RAT LIVER MITOCHONDRIA [J].
BRDICZKA, D ;
PETTE, D ;
BRUNNER, G ;
MILLER, F .
EUROPEAN JOURNAL OF BIOCHEMISTRY, 1968, 5 (02) :294-&
[6]  
CHANCE B, 1956, ADV ENZYMOL REL S BI, V17, P65
[7]  
CRISS WE, 1970, J BIOL CHEM, V245, P6352
[8]  
DAFONCESCAWALKI.F, 1973, Z CHEM KLIN KLIN BIO, V4, P421
[9]   INVIVO AND INVITRO RESPONSE OF HUMAN BRANCHED-CHAIN ALPHA-KETOACID DEHYDROGENASE TO THIAMINE AND THIAMINE PYROPHOSPHATE [J].
DANNER, DJ ;
WHEELER, FB ;
LEMMON, SK ;
ELSAS, LJ .
PEDIATRIC RESEARCH, 1978, 12 (03) :235-238
[10]  
DEVOS MA, 1968, BIOL NEONATORUM, V13, P83