CYSTIC-FIBROSIS .4. ABNORMALITIES OF AIRWAY EPITHELIAL FUNCTION AND THE IMPLICATIONS OF THE DISCOVERY OF THE CYSTIC-FIBROSIS GENE

被引:11
作者
CUTHBERT, AW
机构
[1] Univ. Dept. of Pharmacology
关键词
D O I
10.1136/thx.46.2.124
中图分类号
R56 [呼吸系及胸部疾病];
学科分类号
摘要
[No abstract available]
引用
收藏
页码:124 / 130
页数:7
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共 40 条
[1]   UPTAKE OF [BENZAMIL-H-3 AT DIFFERENT SODIUM CONCENTRATION - INFERENCES REGARDING THE REGULATION OF SODIUM PERMEABILITY [J].
ACEVES, J ;
CUTHBERT, AW .
JOURNAL OF PHYSIOLOGY-LONDON, 1979, 295 (OCT) :491-504
[2]  
BARTHELSON R, 1987, J CLIN INVEST, V80, P179
[3]   CHLORIDE SECRETORY RESPONSE OF CYSTIC-FIBROSIS HUMAN AIRWAY EPITHELIA - PRESERVATION OF CALCIUM BUT NOT PROTEIN-KINASE C-DEPENDENT AND A-DEPENDENT MECHANISMS [J].
BOUCHER, RC ;
CHENG, EHC ;
PARADISO, AM ;
STUTTS, MJ ;
KNOWLES, MR ;
EARP, HS .
JOURNAL OF CLINICAL INVESTIGATION, 1989, 84 (05) :1424-1431
[4]   NA+ TRANSPORT IN CYSTIC-FIBROSIS RESPIRATORY EPITHELIA - ABNORMAL BASAL RATE AND RESPONSE TO ADENYLATE-CYCLASE ACTIVATION [J].
BOUCHER, RC ;
STUTTS, MJ ;
KNOWLES, MR ;
CANTLEY, L ;
GATZY, JT .
JOURNAL OF CLINICAL INVESTIGATION, 1986, 78 (05) :1245-1252
[5]   MECHANISM OF MULTIDRUG RESISTANCE [J].
BRADLEY, G ;
JURANKA, PF ;
LING, V .
BIOCHIMICA ET BIOPHYSICA ACTA, 1988, 948 (01) :87-128
[6]   THAPSIGARGIN, A NEW CALCIUM-DEPENDENT EPITHELIAL ANION SECRETAGOGUE [J].
BRAYDEN, DJ ;
HANLEY, MR ;
THASTRUP, O ;
CUTHBERT, AW .
BRITISH JOURNAL OF PHARMACOLOGY, 1989, 98 (03) :809-816
[7]   INCREASED SULFATION OF GLYCOCONJUGATES BY CULTURED NASAL EPITHELIAL-CELLS FROM PATIENTS WITH CYSTIC-FIBROSIS [J].
CHENG, PW ;
BOAT, TF ;
CRANFILL, K ;
YANKASKAS, JR ;
BOUCHER, RC .
JOURNAL OF CLINICAL INVESTIGATION, 1989, 84 (01) :68-72
[8]   DEFECTIVE INTRACELLULAR-TRANSPORT AND PROCESSING OF CFTR IS THE MOLECULAR-BASIS OF MOST CYSTIC-FIBROSIS [J].
CHENG, SH ;
GREGORY, RJ ;
MARSHALL, J ;
PAUL, S ;
SOUZA, DW ;
WHITE, GA ;
ORIORDAN, CR ;
SMITH, AE .
CELL, 1990, 63 (04) :827-834
[9]   ABNORMAL APICAL CELL-MEMBRANE IN CYSTIC-FIBROSIS RESPIRATORY EPITHELIUM - AN INVITRO ELECTROPHYSIOLOGIC ANALYSIS [J].
COTTON, CU ;
STUTTS, MJ ;
KNOWLES, MR ;
GATZY, JT ;
BOUCHER, RC .
JOURNAL OF CLINICAL INVESTIGATION, 1987, 79 (01) :80-85
[10]   ALTERED SENSITIVITY TO AMILORIDE IN CYSTIC-FIBROSIS - OBSERVATIONS USING CULTURED SWEAT GLANDS [J].
CUTHBERT, AW ;
BRAYDEN, DJ ;
DUNNE, A ;
SMYTH, RL ;
WALLWORK, J .
BRITISH JOURNAL OF CLINICAL PHARMACOLOGY, 1990, 29 (02) :227-234