STABILITY OF FROZEN MUSCLE USED FOR MITOCHONDRIAL ENZYME ASSAYS

被引:2
作者
APPLEGARTH, DA [1 ]
TONG, T [1 ]
CLARKE, LA [1 ]
机构
[1] UNIV BRITISH COLUMBIA,DEPT MED GENET,VANCOUVER V6T 2B5,BC,CANADA
关键词
D O I
10.1007/s004310050107
中图分类号
R72 [儿科学];
学科分类号
100202 ;
摘要
引用
收藏
页码:142 / 142
页数:1
相关论文
共 7 条
[1]   FATAL LACTIC-ACIDOSIS IN INFANCY WITH A DEFECT OF COMPLEX-III OF THE RESPIRATORY-CHAIN [J].
BIRCHMACHIN, MA ;
SHEPHERD, IM ;
WATMOUGH, NJ ;
SHERRATT, HSA ;
BARTLETT, K ;
DARLEYUSMAR, VM ;
MILLIGAN, DWA ;
WELCH, RJ ;
AYNSLEYGREEN, A ;
TURNBULL, DM .
PEDIATRIC RESEARCH, 1989, 25 (05) :553-559
[2]  
COOPERSTEIN SJ, 1951, J BIOL CHEM, V189, P665
[3]   DISPROPORTIONATE DEFICIENCY OF IRON-SULFUR CLUSTERS AND SUBUNITS OF COMPLEX-I IN MITOCHONDRIAL ENCEPHALOMYOPATHY [J].
ICHIKI, T ;
TANAKA, M ;
KOBAYASHI, M ;
SUGIYAMA, N ;
SUZUKI, H ;
NISHIKIMI, M ;
OHNISHI, T ;
NONAKA, I ;
WADA, Y ;
OZAWA, T .
PEDIATRIC RESEARCH, 1989, 25 (02) :194-201
[4]  
KENNAWAY NG, 1984, PEDIATR RES, V18, P991
[5]  
SRERE PA, 1963, ACTA CHEM SCAND, V17, P5129
[6]   PROBLEMS WITH THE BIOCHEMICAL-DIAGNOSIS IN MITOCHONDRIAL (ENCEPHALO)MYOPATHIES [J].
TRIJBELS, JMF ;
SCHOLTE, HR ;
RUITENBEEK, W ;
SENGERS, RCA ;
JANSSEN, AJM ;
BUSCH, HFM .
EUROPEAN JOURNAL OF PEDIATRICS, 1993, 152 (03) :178-184
[7]   EVALUATION OF PROCEDURES FOR ASSAYING OXIDATIVE-PHOSPHORYLATION ENZYME-ACTIVITIES IN MITOCHONDRIAL MYOPATHY MUSCLE BIOPSIES [J].
ZHENG, XX ;
SHOFFNER, JM ;
VOLJAVEC, AS ;
WALLACE, DC .
BIOCHIMICA ET BIOPHYSICA ACTA, 1990, 1019 (01) :1-10