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MEVALONIC ACIDURIA - PATHO-BIOCHEMICAL EFFECTS OF MEVALONATE KINASE-DEFICIENCY ON CHOLESTEROL-METABOLISM IN INTACT FIBROBLASTS
被引:11
作者
:
HOFFMANN, G
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV CALIF SAN DIEGO,DEPT PEDIAT,LA JOLLA,CA 92093
UNIV CALIF SAN DIEGO,DEPT PEDIAT,LA JOLLA,CA 92093
HOFFMANN, G
[
1
]
GIBSON, KM
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV CALIF SAN DIEGO,DEPT PEDIAT,LA JOLLA,CA 92093
UNIV CALIF SAN DIEGO,DEPT PEDIAT,LA JOLLA,CA 92093
GIBSON, KM
[
1
]
NYHAN, WL
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV CALIF SAN DIEGO,DEPT PEDIAT,LA JOLLA,CA 92093
UNIV CALIF SAN DIEGO,DEPT PEDIAT,LA JOLLA,CA 92093
NYHAN, WL
[
1
]
SWEETMAN, L
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV CALIF SAN DIEGO,DEPT PEDIAT,LA JOLLA,CA 92093
UNIV CALIF SAN DIEGO,DEPT PEDIAT,LA JOLLA,CA 92093
SWEETMAN, L
[
1
]
机构
:
[1]
UNIV CALIF SAN DIEGO,DEPT PEDIAT,LA JOLLA,CA 92093
来源
:
JOURNAL OF INHERITED METABOLIC DISEASE
|
1988年
/ 11卷
关键词
:
D O I
:
10.1007/BF01804243
中图分类号
:
R5 [内科学];
学科分类号
:
1002 ;
100201 ;
摘要
:
引用
收藏
页码:229 / 232
页数:4
相关论文
共 6 条
[1]
MEVALONIC ACIDURIA - AN INBORN ERROR OF CHOLESTEROL-BIOSYNTHESIS
BERGER, R
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV GRONINGEN,SCH MED,DEPT NEUROL,9712 KZ GRONINGEN,NETHERLANDS
UNIV GRONINGEN,SCH MED,DEPT NEUROL,9712 KZ GRONINGEN,NETHERLANDS
BERGER, R
SMIT, GPA
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV GRONINGEN,SCH MED,DEPT NEUROL,9712 KZ GRONINGEN,NETHERLANDS
UNIV GRONINGEN,SCH MED,DEPT NEUROL,9712 KZ GRONINGEN,NETHERLANDS
SMIT, GPA
SCHIERBEEK, H
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV GRONINGEN,SCH MED,DEPT NEUROL,9712 KZ GRONINGEN,NETHERLANDS
UNIV GRONINGEN,SCH MED,DEPT NEUROL,9712 KZ GRONINGEN,NETHERLANDS
SCHIERBEEK, H
BIJSTERVELD, K
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV GRONINGEN,SCH MED,DEPT NEUROL,9712 KZ GRONINGEN,NETHERLANDS
UNIV GRONINGEN,SCH MED,DEPT NEUROL,9712 KZ GRONINGEN,NETHERLANDS
BIJSTERVELD, K
LECOULTRE, R
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV GRONINGEN,SCH MED,DEPT NEUROL,9712 KZ GRONINGEN,NETHERLANDS
UNIV GRONINGEN,SCH MED,DEPT NEUROL,9712 KZ GRONINGEN,NETHERLANDS
LECOULTRE, R
[J].
CLINICA CHIMICA ACTA,
1985,
152
(1-2)
: 219
-
222
[2]
BLIGH EG, 1959, CAN J BIOCHEM PHYS, V37, P911
[3]
A RECEPTOR-MEDIATED PATHWAY FOR CHOLESTEROL HOMEOSTASIS
BROWN, MS
论文数:
0
引用数:
0
h-index:
0
BROWN, MS
GOLDSTEIN, JL
论文数:
0
引用数:
0
h-index:
0
GOLDSTEIN, JL
[J].
SCIENCE,
1986,
232
(4746)
: 34
-
47
[4]
BROWN MS, 1978, J BIOL CHEM, V253, P1121
[5]
MEVALONIC ACIDURIA - AN INBORN ERROR OF CHOLESTEROL AND NONSTEROL ISOPRENE BIOSYNTHESIS
HOFFMAN, G
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV CALIF SAN DIEGO,DEPT PEDIAT M009B,LA JOLLA,CA 92093
HOFFMAN, G
GIBSON, KM
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV CALIF SAN DIEGO,DEPT PEDIAT M009B,LA JOLLA,CA 92093
GIBSON, KM
BRANDT, IK
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV CALIF SAN DIEGO,DEPT PEDIAT M009B,LA JOLLA,CA 92093
BRANDT, IK
BADER, PI
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV CALIF SAN DIEGO,DEPT PEDIAT M009B,LA JOLLA,CA 92093
BADER, PI
WAPPNER, RS
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV CALIF SAN DIEGO,DEPT PEDIAT M009B,LA JOLLA,CA 92093
WAPPNER, RS
SWEETMAN, L
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV CALIF SAN DIEGO,DEPT PEDIAT M009B,LA JOLLA,CA 92093
SWEETMAN, L
[J].
NEW ENGLAND JOURNAL OF MEDICINE,
1986,
314
(25)
: 1610
-
1614
[6]
DOLICHOL METABOLISM IN CULTURED SKIN FIBROBLASTS FROM PATIENTS WITH NEURONAL CEROID LIPOFUSCINOSIS (BATTENS DISEASE)
PATON, BC
论文数:
0
引用数:
0
h-index:
0
PATON, BC
POULOS, A
论文数:
0
引用数:
0
h-index:
0
POULOS, A
[J].
JOURNAL OF INHERITED METABOLIC DISEASE,
1984,
7
(03)
: 112
-
116
←
1
→
共 6 条
[1]
MEVALONIC ACIDURIA - AN INBORN ERROR OF CHOLESTEROL-BIOSYNTHESIS
BERGER, R
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV GRONINGEN,SCH MED,DEPT NEUROL,9712 KZ GRONINGEN,NETHERLANDS
UNIV GRONINGEN,SCH MED,DEPT NEUROL,9712 KZ GRONINGEN,NETHERLANDS
BERGER, R
SMIT, GPA
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV GRONINGEN,SCH MED,DEPT NEUROL,9712 KZ GRONINGEN,NETHERLANDS
UNIV GRONINGEN,SCH MED,DEPT NEUROL,9712 KZ GRONINGEN,NETHERLANDS
SMIT, GPA
SCHIERBEEK, H
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV GRONINGEN,SCH MED,DEPT NEUROL,9712 KZ GRONINGEN,NETHERLANDS
UNIV GRONINGEN,SCH MED,DEPT NEUROL,9712 KZ GRONINGEN,NETHERLANDS
SCHIERBEEK, H
BIJSTERVELD, K
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV GRONINGEN,SCH MED,DEPT NEUROL,9712 KZ GRONINGEN,NETHERLANDS
UNIV GRONINGEN,SCH MED,DEPT NEUROL,9712 KZ GRONINGEN,NETHERLANDS
BIJSTERVELD, K
LECOULTRE, R
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV GRONINGEN,SCH MED,DEPT NEUROL,9712 KZ GRONINGEN,NETHERLANDS
UNIV GRONINGEN,SCH MED,DEPT NEUROL,9712 KZ GRONINGEN,NETHERLANDS
LECOULTRE, R
[J].
CLINICA CHIMICA ACTA,
1985,
152
(1-2)
: 219
-
222
[2]
BLIGH EG, 1959, CAN J BIOCHEM PHYS, V37, P911
[3]
A RECEPTOR-MEDIATED PATHWAY FOR CHOLESTEROL HOMEOSTASIS
BROWN, MS
论文数:
0
引用数:
0
h-index:
0
BROWN, MS
GOLDSTEIN, JL
论文数:
0
引用数:
0
h-index:
0
GOLDSTEIN, JL
[J].
SCIENCE,
1986,
232
(4746)
: 34
-
47
[4]
BROWN MS, 1978, J BIOL CHEM, V253, P1121
[5]
MEVALONIC ACIDURIA - AN INBORN ERROR OF CHOLESTEROL AND NONSTEROL ISOPRENE BIOSYNTHESIS
HOFFMAN, G
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV CALIF SAN DIEGO,DEPT PEDIAT M009B,LA JOLLA,CA 92093
HOFFMAN, G
GIBSON, KM
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV CALIF SAN DIEGO,DEPT PEDIAT M009B,LA JOLLA,CA 92093
GIBSON, KM
BRANDT, IK
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV CALIF SAN DIEGO,DEPT PEDIAT M009B,LA JOLLA,CA 92093
BRANDT, IK
BADER, PI
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV CALIF SAN DIEGO,DEPT PEDIAT M009B,LA JOLLA,CA 92093
BADER, PI
WAPPNER, RS
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV CALIF SAN DIEGO,DEPT PEDIAT M009B,LA JOLLA,CA 92093
WAPPNER, RS
SWEETMAN, L
论文数:
0
引用数:
0
h-index:
0
机构:
UNIV CALIF SAN DIEGO,DEPT PEDIAT M009B,LA JOLLA,CA 92093
SWEETMAN, L
[J].
NEW ENGLAND JOURNAL OF MEDICINE,
1986,
314
(25)
: 1610
-
1614
[6]
DOLICHOL METABOLISM IN CULTURED SKIN FIBROBLASTS FROM PATIENTS WITH NEURONAL CEROID LIPOFUSCINOSIS (BATTENS DISEASE)
PATON, BC
论文数:
0
引用数:
0
h-index:
0
PATON, BC
POULOS, A
论文数:
0
引用数:
0
h-index:
0
POULOS, A
[J].
JOURNAL OF INHERITED METABOLIC DISEASE,
1984,
7
(03)
: 112
-
116
←
1
→