PULMONARY VENOOCCLUSIVE DISEASE - FATAL PROGRESSION OF PULMONARY-HYPERTENSION DESPITE STEROID-INDUCED REMISSION OF INTERSTITIAL PNEUMONITIS

被引:16
作者
GILROY, RJ
TEAGUE, MW
LOYD, JE
机构
[1] VANDERBILT UNIV,DEPT MED,DIV PULM & CRIT CARE MED,NASHVILLE,TN 37232
[2] VANDERBILT UNIV,DEPT PATHOL,NASHVILLE,TN 37232
来源
AMERICAN REVIEW OF RESPIRATORY DISEASE | 1991年 / 143卷 / 05期
关键词
D O I
10.1164/ajrccm/143.5_Pt_1.1130
中图分类号
R56 [呼吸系及胸部疾病];
学科分类号
摘要
This report describes a 28-yr-old patient with pulmonary veno-occlusive disease (PVOD). She presented with pulmonary hypertension, hypoxemia, and interstitial pneumonitis. We report the discordance between the response of her hypoxemia and interstitial pneumonitis, which resolved with corticosteroid therapy, and her progressive pulmonary hypertension, which caused fatal right heart failure. This report emphasizes that the radiographic interstitial shadowing of PVOD may be caused by either (1) an inflammatory interstitial pneumonitis (which may be responsive to anti-inflammatory therapy) or (2) interstitial pulmonary edema, or both.
引用
收藏
页码:1130 / 1133
页数:4
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