STUDIES OF PORPHYRIN SYNTHESIS IN FIBROBLASTS OF PATIENTS WITH CONGENITAL ERYTHROPOIETIC PORPHYRIA AND ONE PATIENT WITH HOMOZYGOUS COPROPORPHYRIA

被引：108

作者：

GRANDCHAMP, B ^{[1
]}

DEYBACH, JC ^{[1
]}

GRELIER, M ^{[1
]}

DEVERNEUIL, H ^{[1
]}

NORDMANN, Y ^{[1
]}

机构：

[1] HOP LOUIS MOURIER,FAC MED XAVIER BICHAT,DEPT BIOCHEM,F-92701 COLOMBES,FRANCE

来源：

BIOCHIMICA ET BIOPHYSICA ACTA | 1980年 / 629卷 / 03期

关键词：

D O I：

10.1016/0304-4165(80)90163-4

中图分类号：

Q5 [生物化学]; Q7 [分子生物学];

学科分类号：

071010 ; 081704 ;

摘要：

引用

页码：577 / 586

页数：10

共 19 条

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[7]

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[8] DECREASED LYMPHOCYTE COPROPORPHYRINOGEN-III OXIDASE ACTIVITY IN HEREDITARY COPROPORPHYRIA [J].

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NORDMANN, Y .

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[9]

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[10] ENZYMATIC PROPERTIES OF UROPORPHYRINOGEN 3 COSYNTHETASE [J].

LEVIN, EY .

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