CUTIS MARMORATA TELANGIECTATICA CONGENITA - LONG-TERM FOLLOW-UP, REVIEW OF THE LITERATURE, AND REPORT OF A CASE IN CONJUNCTION WITH CONGENITAL HYPOTHYROIDISM

被引:61
作者
PEHR, K
MOROZ, B
机构
[1] Division of Dermatology, Mcgill University, Montreal Children's Hospital
关键词
D O I
10.1111/j.1525-1470.1993.tb00002.x
中图分类号
R75 [皮肤病学与性病学];
学科分类号
100206 ;
摘要
Cutis marmorata telangiectatica congenita is an uncommon, generally congenital, cutaneous condition. The major skin findings are persistent, fixed cutis marmorata, telangiectasia, and phlebectasia; often, there is associated skin atrophy and ulceration as well. Significantly, two-thirds of patients have other congenital anomalies, although often minor ones. We report a series of eight children with cutis marmorata telangiectatica congenita, including one with associated congenital hypothyroidism, a relationship that has never before been noted.
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页码:6 / 11
页数:6
相关论文
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