NUTRITION IN DYSTROPHIC EPIDERMOLYSIS-BULLOSA

被引：39

作者：

ALLMAN, S ^{[1
]}

HAYNES, L ^{[1
]}

MACKINNON, P ^{[1
]}

ATHERTON, DJ ^{[1
]}

机构：

[1] HOSP SICK CHILDREN,DEPT DIETET,GREAT ORMOND ST,LONDON WC1N 3JH,ENGLAND

来源：

PEDIATRIC DERMATOLOGY | 1992年 / 9卷 / 03期

关键词：

D O I：

10.1111/j.1525-1470.1992.tb00337.x

中图分类号：

R75 [皮肤病学与性病学];

学科分类号：

100206 ;

摘要：

In dystrophic epidermolysis bullosa (EB), a combination of diminished food intake and increased nutritional requirements commonly leads to malnourishment. Adequate nutrition in these patients could provide many benefits, including improved growth, accelerated healing, decreased susceptibility to infection, and enhanced well-being. We assessed nutrition status of children with dystrophic EB, and evaluated the benefits of nutritional advice in those who were considered malnourished. The majority of patients had inadequate intakes of a wide spectrum of nutrients, including those who appeared to be relatively mildly affected. We were unable to secure persisting substantial improvements in dietary intake despite thorough counseling. Adequate nutrition in patients with dystrophic EB depends on active nutritional support starting from birth. The need for more invasive techniques of nourishment, such as nasogastric and gastrostomy feeding, may have to be considered earlier than is currently the case.

引用

页码：231 / 238

页数：8

共 14 条

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