SPLENECTOMY FOR GAUCHERS-DISEASE

被引:26
作者
SALKY, B
KREEL, I
GELERNT, I
BAUER, J
AUFSES, AH
机构
[1] CUNY MT SINAI SCH MED, DEPT SURG, NEW YORK, NY 10029 USA
[2] MT SINAI HOSP & MED CTR, NEW YORK, NY 10029 USA
关键词
D O I
10.1097/00000658-197911000-00006
中图分类号
R61 [外科手术学];
学科分类号
摘要
The records of ten patients who underwent splenectomy for Gaucher's disease were reviewed. All patients had the adult type of the disease. The indications for splenectomy were hypersplenism and mechanical problems. The hematological picture returned to normal in all cases and has remained so throughout the follow-up period. The different forms Gaucher's disease and specific diagnostic tests are discussed. Even though splenectomy is indicated when hematological and mechanical problems exist, selective enzymatic replacement therapy seems to be the preferred future mode of treatment.
引用
收藏
页码:592 / 594
页数:3
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