EPIDERMOLYSIS-BULLOSA ACQUISITA - EFFICACY OF HIGH-DOSE INTRAVENOUS IMMUNOGLOBULINS

被引:60
作者
MEIER, F [1 ]
SONNICHSEN, K [1 ]
SCHAUMBURGLEVER, G [1 ]
DOPFER, R [1 ]
RASSNER, G [1 ]
机构
[1] UNIV TUBINGEN,DEPT PEDIAT,W-7400 TUBINGEN 1,GERMANY
关键词
D O I
10.1016/0190-9622(93)70189-Z
中图分类号
R75 [皮肤病学与性病学];
学科分类号
100206 ;
摘要
A 16-year-old boy had a 6-year history of a generalized bullous eruption that was resistant to multiple therapies. Findings of immunofluorescent split-skin studies and electron microscopy were consistent with a diagnosis of epidermolysis bullosa acquisita. Treatment with cyclosporine and prednisolone decreased new blister formation. Additional therapy with high-dose intravenous immunoglobulins was successful in controlling the patient's disease.
引用
收藏
页码:334 / 337
页数:4
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