DELIRIUM ASSOCIATED WITH JOSEPH DISEASE

被引:9
作者
FUKUTANI, Y
KATSUKAWA, K
MATSUBARA, R
KOBAYASHI, K
NAKAMURA, I
YAMAGUCHI, N
机构
[1] FUKUI MED SCH,DEPT NEUROPSYCHIAT,FUKUI 91011,JAPAN
[2] KANAZAWA UNIV,SCH MED,DEPT NEUROPSYCHIAT,KANAZAWA,ISHIKAWA 920,JAPAN
[3] ISHIKAWA PREFECTURAL TAKAMATSU HOSP,DIV NEUROPSYCHIAT,ISHIKAWA,JAPAN
关键词
D O I
10.1136/jnnp.56.11.1207
中图分类号
R74 [神经病学与精神病学];
学科分类号
摘要
Three Japanese patients with Joseph disease from different families developed sleep disturbance, followed by delirium at the middle to end stage. Brain CT scans of the three patients showed brainstem tegmental atrophy. EEG revealed slowing of background activity. Two necropsy cases showed degeneration of the reticular formation, raphe nuclei and locus ceruleus in the brainstem tegmentum in addition to the common pathological findings of Joseph disease. The clinicopathological correlation between the delirium and the brainstem tegmental atrophy in Joseph disease is discussed.
引用
收藏
页码:1207 / 1212
页数:6
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