ANTINEURONAL (ANTI-RI) ANTIBODIES IN A PATIENT WITH STEROID-RESPONSIVE OPSOCLONUS-MYOCLONUS

被引:81
作者
DROPCHO, EJ
KLINE, LB
RISER, J
机构
[1] UNIV ALABAMA,DEPT OPHTHALMOL,BIRMINGHAM,AL 35294
[2] BIRMINGHAM VET AFFAIRS MED CTR,BIRMINGHAM,AL
[3] BROOKWOOD MED CTR,BIRMINGHAM,AL
关键词
D O I
10.1212/WNL.43.1_Part_1.207
中图分类号
R74 [神经病学与精神病学];
学科分类号
摘要
A 45-year-old woman developed opsoclonus, myoclonus, and severe truncal and gait ataxia. Serum and CSF contained IgG antibodies that appear to be identical to ''anti-Ri'' antibodies associated with paraneoplastic opsoclonus and ataxia. The patient had a fluctuating course with exacerbations that responded well to corticosteroids and later to cyclophosphamide. Her anti-Ri antibody titer has declined significantly but still remains high. After more than 3 years of follow-up, no neoplasm has been detected.
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页码:207 / 211
页数:5
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