MALE PSEUDOHERMAPHRODITISM DUE TO NONSALT-LOSING 3-BETA-HYDROXYSTEROID DEHYDROGENASE-DEFICIENCY - GENDER ROLE CHANGE AND ABSENCE OF GYNECOMASTIA AT PUBERTY

被引:44
作者
MENDONCA, BB
BLOISE, W
ARNHOLD, IJP
BATISTA, MC
TOLEDO, SPA
DRUMMOND, MCF
NICOLAU, W
MATTAR, E
机构
关键词
D O I
10.1016/0022-4731(87)90396-7
中图分类号
Q5 [生物化学]; Q7 [分子生物学];
学科分类号
071010 ; 081704 ;
摘要
引用
收藏
页码:669 / 675
页数:7
相关论文
共 24 条
[1]  
ABRAHAM GE, 1974, ACTA ENDOCR-COP S183, V75, P1
[2]   URINARY EXCRETION OF PREGNANETRIOL AND DELTA-5-PREGNENETRIOL IN 2 FORMS OF CONGENITAL ADRENAL HYPERPLASIA [J].
BONGIOVA.AM ;
EBERLEIN, WR ;
MOSHANG, T .
JOURNAL OF CLINICAL INVESTIGATION, 1971, 50 (12) :2751-&
[4]  
BONGIOVANNI AM, 1981, FERTIL STERIL, V35, P599
[5]   ADRENOGENITAL SYNDROME WITH DEFICIENCY OF 3BETA-HYDROXYSTEROID DEHYDROGENASE [J].
BONGIOVANNI, AM .
JOURNAL OF CLINICAL INVESTIGATION, 1962, 41 (11) :2086-&
[6]  
DEPERETTI E, 1980, ADRENAL ANDROGENS, P141
[7]   FAMILIAL MALE PSEUDOHERMAPHRODITISM WITHOUT GYNECOMASTIA DUE TO DEFICIENT TESTICULAR 17-KETOSTEROID REDUCTASE-ACTIVITY [J].
GIVENS, JR ;
WISER, WL ;
SUMMITT, RL ;
KERBER, IJ ;
ANDERSEN, RN ;
PITTAWAY, DE ;
FISH, SA .
NEW ENGLAND JOURNAL OF MEDICINE, 1974, 291 (18) :938-944
[8]  
GOLDMAN AS, 1972, P SOC EXP BIOL MED, V140, P1486
[9]   MALE PSEUDOHERMAPHRODITISM SECONDARY TO 17-BETA-HYDROXYSTEROID DEHYDROGENASE-DEFICIENCY - GENDER ROLE CHANGE WITH PUBERTY [J].
IMPERATOMCGINLEY, J ;
PETERSON, RE ;
STOLLER, R ;
GOODWIN, WE .
JOURNAL OF CLINICAL ENDOCRINOLOGY & METABOLISM, 1979, 49 (03) :391-395
[10]   ANDROGENS AND THE EVOLUTION OF MALE-GENDER IDENTITY AMONG MALE PSEUDO-HERMAPHRODITES WITH 5-ALPHA-REDUCTASE DEFICIENCY [J].
IMPERATOMCGINLEY, J ;
PETERSON, RE ;
GAUTIER, T ;
STURLA, E .
NEW ENGLAND JOURNAL OF MEDICINE, 1979, 300 (22) :1233-1237