MUSCULAR PSEUDOHYPERTROPHY IN AN ADULT CASE WITH CENTRONUCLEAR MYOPATHY

被引:7
作者
MATSUSHITA, S
IKEDA, S
HANYU, N
YAMAMOTO, K
YANAGISAWA, N
机构
[1] SHINSHU UNIV,SCH MED,DEPT MED NEUROL,MATSUMOTO,NAGANO 390,JAPAN
[2] NAGANO RED CROSS HOSP,DEPT NEUROL,NAGANO,JAPAN
关键词
CENTRONUCLEAR MYOPATHY; MUSCULAR PSEUDOHYPERTROPHY;
D O I
10.1159/000116671
中图分类号
R74 [神经病学与精神病学];
学科分类号
摘要
We describe a 40-year-old male case with centronuclear myopathy showing a unique clinical picture of generalized muscular pseudohypertrophy. CT scan, ultrasound imaging and histopathological studies of muscles revealed that muscle enlargement in this case might be caused by marked intrafascicular fatty infiltration. It is suggested that muscular pseudohypertrophy may occur in adult centronuclear myopathy cases with a long clinical course and that CT and ultrasound scans are very useful for the evaluation of diseased muscles.
引用
收藏
页码:172 / 174
页数:3
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