URIDINE DIPHOSPHO-N-ACETYLGALACTOSAMINE-4-SULFATE SULFOHYDROLASE ACTIVITY OF HUMAN ARYLSULFATASE-B AND ITS DEFICIENCY IN MAROTEAUX-LAMY SYNDROME

被引：80

作者：

FLUHARTY, AL ^{[1
]}

STEVENS, RL ^{[1
]}

FUNG, D ^{[1
]}

PEAK, S ^{[1
]}

KIHARA, H ^{[1
]}

机构：

[1] PACIFIC STATE HOSP, NEUROPSYCHIAT INST, RES GRP, POB 100-R, POMONA, CA 91766 USA

来源：

BIOCHEMICAL AND BIOPHYSICAL RESEARCH COMMUNICATIONS | 1975年 / 64卷 / 03期

关键词：

D O I：

10.1016/0006-291X(75)90140-0

中图分类号：

Q5 [生物化学]; Q7 [分子生物学];

学科分类号：

071010 ; 081704 ;

摘要：

引用

收藏

页码：955 / 962

页数：8

相关论文

共 16 条

[1] THE ASSAY OF ARYLSULPHATASE-A AND ARYLSULPHATASE-B IN HUMAN URINE
BAUM, H
DODGSON, KS
SPENCER, B
[J]. CLINICA CHIMICA ACTA, 1959, 4 (03) : 453 - 455
[2] BERATIS NG, 1974, AM J HUM GENET, V26, pA12
[3] DORFMAN A, 1972, METABOLIC BASIS INHE, P1218
[4] FERRANTE ND, 1974, JOHNS HOPKINS MED J, V135, P42
[5] ARYLSULFATASE-B DEFICIENCY IN MAROTEAUX-LAMY SYNDROME CULTURED FIBROBLASTS
FLUHARTY, AL
STEVENS, RL
SANDERS, DL
KIHARA, H
[J]. BIOCHEMICAL AND BIOPHYSICAL RESEARCH COMMUNICATIONS, 1974, 59 (02) : 455 - 461
[6] DEFECT IN HURLERS AND HUNTERS SYNDROMES - FAULTY DEGRADATION OF MUCOPOLYSACCHARIDE
FRATANTONI, JC
HALL, CW
NEUFELD, EF
[J]. PROCEEDINGS OF THE NATIONAL ACADEMY OF SCIENCES OF THE UNITED STATES OF AMERICA, 1968, 60 (02) : 699 - +
[7] KELLY TE, 1974, AM J HUM GENET, V26, pA48
[8] LOWRY OH, 1951, J BIOL CHEM, V193, P265
[9] DEFICIENCY OF CHONDROITIN SULFATE N-ACETYLGALACTOSAMINE 4-SULFATE SULFATASE IN MAROTEAUX-LAMY SYNDROME
MATALON, R
ARBOGAST, B
DORFMAN, A
[J]. BIOCHEMICAL AND BIOPHYSICAL RESEARCH COMMUNICATIONS, 1974, 61 (04) : 1450 - 1457
[10] MAROTEAUX-LAMY DISEASE (MUCOPOLYSACCHARIDOSIS-VI) SUBTYPE-A - DEFICIENCY OF A N-ACETYLGALACTOSAMINE-4-SULFATASE
OBRIEN, JF
CANTZ, M
SPRANGER, J
[J]. BIOCHEMICAL AND BIOPHYSICAL RESEARCH COMMUNICATIONS, 1974, 60 (03) : 1170 - 1177