THE OCCURRENCE OF C-6-C-10-DICARBOXYLIC ACIDS IN URINE FROM PATIENTS AND RATS TREATED WITH DIPROPYLACETATE

被引:43
作者
MORTENSEN, PB
GREGERSEN, N
KOLVRAA, S
CHRISTENSEN, E
机构
[1] AARHUS UNIV,AARHUS KOMMUNE HOSP,INST HUMAN GENET,DK-8000 AARHUS C,DENMARK
[2] RIGSHOSP,DEPT PEDIAT,CLIN GENET SECT,DK-2100 COPENHAGEN O,DENMARK
[3] RIGSHOSP,DEPT OBSTET & GYNAECOL,DK-2100 COPENHAGEN O,DENMARK
来源
BIOCHEMICAL MEDICINE | 1980年 / 24卷 / 02期
关键词
D O I
10.1016/0006-2944(80)90006-X
中图分类号
Q5 [生物化学]; Q7 [分子生物学];
学科分类号
071010 ; 081704 ;
摘要
引用
收藏
页码:153 / 161
页数:9
相关论文
共 20 条
  • [1] OMEGA-OXIDATION OF STEARIC ACID IN NORMAL, STARVED AND DIABETIC RAT-LIVER
    BJORKHEM, I
    [J]. EUROPEAN JOURNAL OF BIOCHEMISTRY, 1973, 40 (02): : 415 - 422
  • [2] CAMFIELD PR, 1979, LANCET, V1, P1198
  • [3] Dicarboxylic Aciduria as an Indicator of Defective beta-Oxidation in Twin Siblings with a Vomiting Sickness and Hypoglycaemia Similar to Jamaican Vomiting Sickness
    Chalmers, Ronald A.
    Lawson, Alexander M.
    [J]. BIOCHEMICAL SOCIETY TRANSACTIONS, 1978, 6 : 111 - 113
  • [4] REYE-LIKE SYNDROME ASSOCIATED WITH VALPROIC ACID THERAPY
    GERBER, N
    DICKINSON, RG
    HARLAND, RC
    LYNN, RK
    HOUGHTON, D
    ANTONIAS, JI
    SCHIMSCHOCK, JC
    [J]. JOURNAL OF PEDIATRICS, 1979, 95 (01) : 142 - 144
  • [5] NON-KETOTIC C6-C10-DICARBOXYLIC ACIDURIA - BIOCHEMICAL INVESTIGATIONS OF 2 CASES
    GREGERSEN, N
    ROSLEFF, F
    KOLVRAA, S
    HOBOLTH, N
    RASMUSSEN, K
    LAURITZEN, R
    [J]. CLINICA CHIMICA ACTA, 1980, 102 (2-3) : 179 - 189
  • [6] SPECIFIC AND SENSITIVE METHOD FOR THE DETERMINATION OF C6-C10 DICARBOXYLIC-ACIDS IN SERUM AND URINE BY SELECTED ION MONITORING
    GREGERSEN, N
    [J]. JOURNAL OF CHROMATOGRAPHY, 1979, 162 (03): : 377 - 381
  • [7] SUBERYLGLYCINE EXCRETION IN URINE FROM A PATIENT WITH DICARBOXYLIC ACIDURIA
    GREGERSEN, N
    LAURITZEN, R
    RASMUSSEN, K
    [J]. CLINICA CHIMICA ACTA, 1976, 70 (03) : 417 - 425
  • [8] METABOLISM OF BRANCHED MEDIUM CHAIN-LENGTH FATTY-ACID .1. OMEGA-OXIDATION OF SODIUM DIPROPYLACETATE IN RATS
    KUHARA, T
    MATSUMOTO, I
    [J]. BIOMEDICAL MASS SPECTROMETRY, 1974, 1 (04): : 291 - 294
  • [9] METABOLISM OF BRANCHED MEDIUM CHAIN-LENGTH FATTY-ACID .2. BETA-OXIDATION OF SODIUM DIPROPYLACETATE IN RATS
    MATSUMOTO, I
    KUHARA, T
    YOSHINO, M
    [J]. BIOMEDICAL MASS SPECTROMETRY, 1976, 3 (05): : 235 - 240
  • [10] MATSUMOTO J, 1976, ADV MASS SPECTROM, V1, P17