STUDIES ON PROLIDASE DEFICIENCY WITH A POSSIBLE DEFECT IN COLLAGEN-METABOLISM

被引:12
作者
ISEMURA, M
HANYU, T
ONO, T
IGARASHI, R
SATO, Y
GEJYO, F
NAKAZAWA, R
MIYAKAWA, T
TAKAGI, T
KUBOKI, Y
SASAKI, S
机构
[1] NIIGATA UNIV, SCH MED, DEPT BIOCHEM, NIIGATA 951, JAPAN
[2] NIIGATA UNIV, SCH MED, DEPT DERMATOL, NIIGATA 951, JAPAN
[3] NIIGATA UNIV, SCH MED, DEPT INTERNAL MED, NIIGATA 951, JAPAN
[4] TOKYO MED & DENT UNIV, SCH DENT, DEPT BIOCHEM, TOKYO 113, JAPAN
关键词
D O I
10.1620/tjem.134.21
中图分类号
R5 [内科学];
学科分类号
1002 ; 100201 ;
摘要
引用
收藏
页码:21 / 28
页数:8
相关论文
共 17 条
[1]   PROLIDASE DEFICIENCY - DERMATOLOGICAL MANIFESTATIONS AND SOME ADDITIONAL BIOCHEMICAL STUDIES [J].
ARATA, J ;
UMEMURA, S ;
YAMAMOTO, Y ;
HAGIYAMA, M ;
NOHARA, N .
ARCHIVES OF DERMATOLOGY, 1979, 115 (01) :62-67
[2]   URINARY-EXCRETION OF FREE HYDROXYLYSINE, PEPTIDE-BOUND HYDROXYLYSINE AND HYDROXYLYSYL GLYCOSIDES IN PHYSIOLOGICAL CONDITIONS [J].
ASKENASI, R .
CLINICA CHIMICA ACTA, 1975, 59 (01) :87-92
[3]   CHARACTERIZATION OF COLLAGEN OF HUMAN HYPERTROPHIC AND NORMAL SCARS [J].
BAILEY, AJ ;
BAZIN, S ;
SIMS, TJ ;
LELOUS, M ;
NICOLETIS, C ;
DELAUNAY, A .
BIOCHIMICA ET BIOPHYSICA ACTA, 1975, 405 (02) :412-421
[4]   COMPARISON BETWEEN REDUCIBLE INTERMOLECULAR CROSSLINKS OF COLLAGENS FROM MATURE DERMIS AND YOUNG DERMAL SCAR TISSUE OF GUINEA-PIG [J].
FORREST, L ;
MECHANIC, GL ;
SHUTTLEW.A ;
JACKSON, DS .
BIOCHEMICAL AND BIOPHYSICAL RESEARCH COMMUNICATIONS, 1972, 46 (05) :1776-&
[5]  
GEJYO F, 1980, J JAP SOC INTERN MED, V69, P59
[6]   A SYNDROME RESEMBLING LATHYRISM ASSOCIATED WITH IMINODIPEPTIDURIA [J].
GOODMAN, SI ;
SOLOMONS, CC ;
MUSCHENHEIM, F ;
MCINTYRE, CA ;
MILES, B ;
OBRIEN, D .
AMERICAN JOURNAL OF MEDICINE, 1968, 45 (01) :152-+
[7]  
HANYU T, 1979, CONNECT TISSUE, V11, P55
[8]   PROLIDASE DEFICIENCY WITH IMIDODIPEPTIDURIA - FAMILIAL CASE WITH AND WITHOUT CLINICAL SYMPTOMS [J].
ISEMURA, M ;
HANYU, T ;
GEJYO, F ;
NAKAZAWA, R ;
IGARASHI, R ;
MATSUO, S ;
IKEDA, K ;
SATO, Y .
CLINICA CHIMICA ACTA, 1979, 93 (03) :401-407
[9]   COMPARATIVE-STUDY OF CARBOHYDRATE-PROTEIN COMPLEXES .2. DETERMINATION OF HYDROXYLYSINE AND ITS GLYCOSIDES IN HUMAN-SKIN AND SCAR COLLAGENS BY AN IMPROVED METHOD [J].
ISEMURA, M ;
TAKAHASHI, K ;
IKENAKA, T .
JOURNAL OF BIOCHEMISTRY, 1976, 80 (04) :653-658
[10]  
ISEMURA M, 1976, NIIGATA MED J, V90, P351