LIVER-TRANSPLANTATION AND HEMOPHILIA-A

被引:19
作者
LERUT, JP
LATERRE, PF
LAVENNEPARDONGE, E
DONATACCIO, M
GEUBEL, A
REYNAERT, MS
OTTE, JB
机构
[1] UNIV CATHOLIQUE LOUVAIN,ST LUC UNIV HOSP,DEPT INTENS CARE,B-1200 BRUSSELS,BELGIUM
[2] UNIV CATHOLIQUE LOUVAIN,ST LUC UNIV HOSP,HAEMOSTASIS UNIT,B-1200 BRUSSELS,BELGIUM
[3] UNIV CATHOLIQUE LOUVAIN,ST LUC UNIV HOSP,DEPT GASTROENTEROL,B-1200 BRUSSELS,BELGIUM
来源
JOURNAL OF HEPATOLOGY | 1995年 / 22卷 / 05期
关键词
HEMOPHILIA A; HEMOPHILIA B; INHERITED METABOLIC DISEASE; LIVER TRANSPLANTATION; METABOLIC CURE;
D O I
10.1016/0168-8278(95)80454-4
中图分类号
R57 [消化系及腹部疾病];
学科分类号
摘要
Liver transplantation has become the standard treatment for a variety of inherited metabolic disorders. We report on two patients who underwent successful transplantation for posthepatitis viral cirrhosis, which developed following blood factor replacement for haemophilia A. The second patient was transplanted before the occurrence of major complications of either his liver or haemophilic disease. We propose early liver transplantation to achieve metabolic cure of haemophilia.
引用
收藏
页码:583 / 585
页数:3
相关论文
共 22 条
[1]  
BONTEMPO FA, 1987, BLOOD, V69, P1721
[2]   FACTOR-XI DEFICIENCY ACQUIRED BY LIVER-TRANSPLANTATION [J].
CLARKSON, K ;
ROSENFELD, B ;
FAIR, J ;
KLEIN, A ;
BELL, W .
ANNALS OF INTERNAL MEDICINE, 1991, 115 (11) :877-879
[3]   ORTHOTOPIC LIVER-TRANSPLANTATION IN A PATIENT WITH COMBINED HEMOPHILIA-A AND HEMOPHILIA-B [J].
DELORME, MA ;
ADAMS, PC ;
GRANT, D ;
GHENT, CN ;
WALKER, IR ;
WALL, WJ .
AMERICAN JOURNAL OF HEMATOLOGY, 1990, 33 (02) :136-138
[4]  
DONATACCIO M, 1994, TRANSPLANT P, V26, P3588
[5]  
DZIK WH, 1987, NEW ENGL J MED, V316, P1217
[6]  
FRIEND PJ, 1993, NEW ENGL J MED, V323, P807
[7]   CURE OF HEMOPHILIA-A BY ORTHOTOPIC LIVER-TRANSPLANTATION [J].
GIBAS, A ;
DIENSTAG, JL ;
SCHAFER, AI ;
DELMONICO, F ;
BYNUM, TE ;
SCHOOLEY, R ;
RUBIN, RH ;
COSIMI, AB .
GASTROENTEROLOGY, 1988, 95 (01) :192-194
[8]   HEMOPHILIA - ROLE OF ORGAN HOMOGRAFTS [J].
MARCHIORO, TL ;
HOUGIE, C ;
RAGDE, H ;
EPSTEIN, RB ;
THOMAS, ED .
SCIENCE, 1969, 163 (3863) :188-+
[9]  
MEILI EO, 1989, SCHWEIZ MED WSCHR, V119, P1332
[10]  
MERION RM, 1988, SURGERY, V104, P929