TYPE 2 HYPERPROLINEMIA - ABSENCE OF DELTA-1-PYRROLINE-5-CARBOXYLIC ACID DEHYDROGENASE-ACTIVITY

被引：37

作者：

VALLE, DL

PHANG, JM

GOODMAN, SI

机构：

[1] NCI,METAB BRANCH,BETHESDA,MD 20014

[2] UNIV COLORADO,MED CTR,DEPT PEDIAT,4200 E 9TH AVE,DENVER,CO 80220

来源：

关键词：

D O I：

10.1126/science.185.4156.1053

中图分类号：

O [数理科学和化学]; P [天文学、地球科学]; Q [生物科学]; N [自然科学总论];

学科分类号：

07 ; 0710 ; 09 ;

摘要：

引用

页码：1053 / 1054

页数：2

共 11 条

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EFRON, ML
[J]. NEW ENGLAND JOURNAL OF MEDICINE, 1965, 272 (24) : 1243 - +
[3] GOODMAN SA, IN PRESS
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PHANG, JM
DOWNING, SJ
VALLE, D
[J]. ANALYTICAL BIOCHEMISTRY, 1973, 55 (01) : 266 - 271
[8] RADIOISOTOPIC ASSAY FOR ORNITHINE-DELTA-TRANSAMINASE
PHANG, JM
DOWNING, SJ
VALLE, D
[J]. ANALYTICAL BIOCHEMISTRY, 1973, 55 (01) : 272 - 277
[9] PHANG JM, UNPUBLISHED RESULTS
[10] SCRIVER CR, 1972, METABOLIC BASIS INHE