PATENT DUCTUS VENOSUS WITH HYPOPLASTIC RIGHT HEPATOPORTAL SYSTEM IN A YOUNG-CHILD BORN WITH ASYMMETRIC INTRAUTERINE GROWTH-RETARDATION

被引:34
作者
MAISAWA, S [1 ]
TAKASAGO, Y [1 ]
OYAKE, Y [1 ]
MAETA, H [1 ]
FUJIWARA, T [1 ]
机构
[1] IWATE MED UNIV,DEPT PAEDIAT,MORIOKA,IWATE 020,JAPAN
关键词
PATENT DUCTUS VENOSUS; GALACTOSEMIA; HYPERAMMONEMIA; ASYMMETRIC INTRAUTERINE GROWTH RETARDATION;
D O I
10.1007/BF01957722
中图分类号
R72 [儿科学];
学科分类号
100202 ;
摘要
We report a functioning ductus venosus with hypoplasia of the right hepatoportal system in a 2-year-old child born with asymmetric intra-uterine growth retardation. Postprandial galactosaemia and hyperammonaemia were clues to diagnosis of portal-systemic shunt through the patent ductus venosus, which was confirmed by ultrasonography and angiography.
引用
收藏
页码:569 / 571
页数:3
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