PYROGLUTAMIC ACIDURIA - STUDIES ON ENZYMIC BLOCK AND ON METABOLIC ORIGIN OF PYROGLUTAMIC ACID

被引:51
作者
ELDJARN, L
STOKKE, O
JELLUM, E
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D O I
10.1016/0009-8981(72)90359-2
中图分类号
R446 [实验室诊断]; R-33 [实验医学、医学实验];
学科分类号
1001 ;
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页码:461 / &
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共 15 条
[1]  
BESSMAN SP, 1948, J BIOL CHEM, V175, P817
[2]   ENZYMIC FORMATION OF PYRROLIDONE CARBOXYLIC ACID FROM GAMMA-GLUTAMYL PEPTIDES [J].
CONNELL, GE ;
HANES, CS .
NATURE, 1956, 177 (4504) :377-378
[3]   PYROGLUTAMIC ACIDURIA - A NEW INBORN ERROR OF METABOLISM [J].
JELLUM, E ;
KLUGE, T ;
BORRESEN, HC ;
STOKKE, O ;
ELDJARN, L .
SCANDINAVIAN JOURNAL OF CLINICAL & LABORATORY INVESTIGATION, 1970, 26 (04) :327-&
[4]   SCREENING FOR METABOLIC DISORDERS USING GAS-LIQUID CHROMATOGRAPHY, MASS SPECTROMETRY, AND COMPUTER TECHNIQUE [J].
JELLUM, E ;
STOKKE, O ;
ELDJARN, L .
SCANDINAVIAN JOURNAL OF CLINICAL & LABORATORY INVESTIGATION, 1971, 27 (03) :273-&
[5]   A GAS-LIQUID CHROMATOGRAPHIC METHOD FOR DETERMINATION OF PHENYLALANINE IN SERUM [J].
JELLUM, E ;
CLOSE, VA ;
PATTON, W ;
PEREIRA, W ;
HALPERN, B .
ANALYTICAL BIOCHEMISTRY, 1969, 31 (1-3) :227-&
[6]  
KLUGE T, 1972, SURGERY, V71, P104
[7]  
KRISHNASWAMY PR, 1962, J BIOL CHEM, V237, P2932
[8]   REGULATION OF AMMONIA EXCRETION IN THE RAT [J].
LEONARD, E ;
ORLOFF, J .
AMERICAN JOURNAL OF PHYSIOLOGY, 1955, 182 (01) :131-138
[9]   ENERGY PRODUCTION + PYRROLIDONECARBOXYLIC ACID FORMATION IN RAT LIVER NUCLEI [J].
NIWAGUCHI, T ;
STRECKER, HJ .
BIOCHEMICAL AND BIOPHYSICAL RESEARCH COMMUNICATIONS, 1964, 16 (06) :535-&
[10]   GAMMA-GLUTAMYL CYCLE - A POSSIBLE TRANSPORT SYSTEM FOR AMINO ACIDS [J].
ORLOWSKI, M ;
MEISTER, A .
PROCEEDINGS OF THE NATIONAL ACADEMY OF SCIENCES OF THE UNITED STATES OF AMERICA, 1970, 67 (03) :1248-&