ABNORMAL LYSOSOMAL CATHEPSIN ACTIVITIES IN LEUKOCYTES AND CULTURED SKIN FIBROBLASTS IN LATE INFANTILE, BUT NOT IN JUVENILE NEURONAL CEROID-LIPOFUSCINOSIS (BATTEN DISEASE)

被引:10
作者
BENNETT, MJ
CHERN, L
CARPENTER, KH
SLADKY, JT
机构
[1] CHILDRENS HOSP, DEPT PEDIAT, PHILADELPHIA, PA 19104 USA
[2] CHILDRENS HOSP, DEPT CHEM PATHOL, SHEFFIELD S10 2TH, S YORKSHIRE, ENGLAND
关键词
NEURONAL CEROID-LIPOFUSCINOSIS; BATTEN DISEASE; CATHEPSINS; LYSOSOMAL PROTEASES;
D O I
10.1016/0009-8981(92)90028-O
中图分类号
R446 [实验室诊断]; R-33 [实验医学、医学实验];
学科分类号
1001 ;
摘要
[No abstract available]
引用
收藏
页码:111 / 117
页数:7
相关论文
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