AORTIC REGURGITATION AND ANEURYSM OF SINUS OF VALSALVA ASSOCIATED WITH OSTEOGENESIS IMPERFECTA

被引:14
作者
OHTEKI, H
OHTSUBO, S
SAKURAI, J
KOGA, N
KOHCHI, K
ITOH, T
机构
[1] KOGA HOSP,DEPT CARDIOL,SAGA,JAPAN
[2] SAGA MED SCH,DEPT THORAC & CARDIOVASC SURG,SAGA 84001,JAPAN
关键词
OSTEOGENESIS IMPERFECTA; ANNULOAORTIC ECTASIA; AORTIC ROOT RECONSTRUCTION;
D O I
10.1055/s-2007-1019989
中图分类号
R5 [内科学];
学科分类号
1002 ; 100201 ;
摘要
A case of osteogenesis imperfecta with aortic regurgitation is described. The patient had a dilated aortic valve ring and an aneurysm of the Sinus of Valsalva. The patient manifested severe hemodynamic abnormalities and underwent aortic root reconstruction using a valved conduit. The operative problems and the pathological findings are discussed.
引用
收藏
页码:294 / 295
页数:2
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