IDENTIFICATION OF 4,6-DIOXOHEPTANOIC ACID (SUCCINYLACETONE), 3,5-DIOXOOCTANEDIOIC ACID (SUCCINYLACETOACETATE) AND 4-OXO-6-HYDROXYHEPTANOIC ACID IN THE URINE FROM PATIENTS WITH HEREDITARY TYROSINEMIA

被引:18
作者
LINDBLAD, B [1 ]
STEEN, G [1 ]
机构
[1] GOTHENBURG UNIV,DEPT CLIN CHEM,S-41345 GOTHENBURG,SWEDEN
来源
BIOMEDICAL MASS SPECTROMETRY | 1982年 / 9卷 / 10期
关键词
D O I
10.1002/bms.1200091003
中图分类号
R318 [生物医学工程];
学科分类号
0831 ;
摘要
引用
收藏
页码:419 / 424
页数:6
相关论文
共 8 条
[1]   DEFICIENCY OF FUMARYLACETOACETASE IN A PATIENT WITH HEREDITARY TYROSINEMIA [J].
BERGER, R ;
SMIT, GPA ;
STOKERDEVRIES, SA ;
DURAN, M ;
KETTING, D ;
WADMAN, SK .
CLINICA CHIMICA ACTA, 1981, 114 (01) :37-44
[2]   URINARY-EXCRETION OF SUCCINYLACETONE AND DELTA-AMINOLEVULINIC-ACID IN PATIENTS WITH HEREDITARY TYROSINEMIA [J].
CHRISTENSEN, E ;
JACOBSEN, BB ;
GREGERSEN, N ;
HJEDS, H ;
PEDERSEN, JB ;
BRANDT, NJ ;
BAEKMARK, UB .
CLINICA CHIMICA ACTA, 1981, 116 (03) :331-341
[3]  
DEBOER TJ, 1963, ORG SYNTH, V4, P250
[4]   ON THE RENAL TUBULAR DAMAGE IN HEREDITARY TYROSINEMIA AND ON THE FORMATION OF SUCCINYLACETOACETATE AND SUCCINYLACETONE [J].
FALLSTROM, SP ;
LINDBLAD, B ;
STEEN, G .
ACTA PAEDIATRICA SCANDINAVICA, 1981, 70 (03) :315-320
[5]  
FALLSTROM SP, 1979, PEDIATR RES, V13, P78, DOI 10.1203/00006450-197901000-00056
[6]   ASSAY, PROPERTIES AND TISSUE DISTRIBUTION OF PARA HYDROXYPHENYLPYRUVATE HYDROXYLASE [J].
FELLMAN, JH ;
ROTH, ES ;
FUJITA, TS .
BIOCHIMICA ET BIOPHYSICA ACTA, 1972, 284 (01) :90-&
[7]   ENZYMIC DEFECTS IN HEREDITARY TYROSINEMIA [J].
LINDBLAD, B ;
LINDSTEDT, S ;
STEEN, G .
PROCEEDINGS OF THE NATIONAL ACADEMY OF SCIENCES OF THE UNITED STATES OF AMERICA, 1977, 74 (10) :4641-4645
[8]   PREPARATION OF 2-ACETYLCYCLOPENT-4-ENE-1,3-DIONES FROM MALEIC ANHYDRIDES + ISOPROPENYL ACETATE [J].
NILSSON, M .
ACTA CHEMICA SCANDINAVICA, 1964, 18 (02) :441-&