PURIFICATION, BIOCHEMICAL AND IMMUNOLOGICAL CHARACTERIZATION OF HEXOSAMINIDASE-A FROM VARIANT AB OF INFANTILE GM2 GANGLIOSIDOSIS

被引:29
作者
CONZELMANN, E [1 ]
SANDHOFF, K [1 ]
NEHRKORN, H [1 ]
GEIGER, B [1 ]
ARNON, R [1 ]
机构
[1] WEIZMANN INST SCI, DEPT CHEM IMMUNOL, REHOVOT, ISRAEL
来源
EUROPEAN JOURNAL OF BIOCHEMISTRY | 1978年 / 84卷 / 01期
关键词
D O I
10.1111/j.1432-1033.1978.tb12137.x
中图分类号
Q5 [生物化学]; Q7 [分子生物学];
学科分类号
071010 ; 081704 ;
摘要
引用
收藏
页码:27 / 33
页数:7
相关论文
共 27 条
[1]   GM2-GANGLIOSIDOSIS, AB VARIANT - CLINICOPATHOLOGICAL STUDY OF A CASE [J].
BAECQUE, CMD ;
SUZUKI, K ;
RAPIN, I ;
JOHNSON, AB ;
WHETHERS, DL ;
SUZUKI, K .
ACTA NEUROPATHOLOGICA, 1975, 33 (03) :207-226
[2]   ANTIBODY-MEDIATED THERMAL STABILIZATION OF HUMAN HEXOSAMINIDASES [J].
BENYOSEPH, Y ;
GEIGER, B ;
ARNON, R .
IMMUNOCHEMISTRY, 1975, 12 (03) :221-226
[3]   SUBUNIT STRUCTURE OF HUMAN HEXOSAMINIDASE VERIFIED - INTERCONVERTIBILITY OF HEXOSAMINIDASE ISOENZYMES [J].
BEUTLER, E ;
KUHL, W .
NATURE, 1975, 258 (5532) :262-264
[4]   LATE ONSET GM2-GANGLIOSIDOSIS - CLINICAL, PATHOLOGICAL, AND BIOCHEMICAL STUDIES ON 8 PATIENTS [J].
BRETT, EM ;
ELLIS, RB ;
HAAS, L ;
IKONNE, JU ;
LAKE, BD ;
PATRICK, AD ;
STEPHENS, R .
ARCHIVES OF DISEASE IN CHILDHOOD, 1973, 48 (10) :775-785
[5]   CHEMICAL CHARACTERIZATION AND SUBUNIT STRUCTURE OF HUMAN N-ACETYLHEXOSAMINIDASES-A AND ACETYLHEXOSAMINIDASES-B [J].
GEIGER, B ;
ARNON, R .
BIOCHEMISTRY, 1976, 15 (16) :3484-3493
[6]   SPECIFIC DETERMINATION OF N-ACETYL-BETA-D-HEXOSAMINIDASE ISOZYME-A AND ISOZYME-B BY RADIOIMMUNOASSAY AND RADIAL IMMUNODIFFUSION [J].
GEIGER, B ;
NAVON, R ;
BENYOSEPH, Y ;
ARNON, R .
EUROPEAN JOURNAL OF BIOCHEMISTRY, 1975, 56 (01) :311-318
[7]  
HARZER K, 1970, Z ANAL CHEM FRESENIU, V252, P170
[9]  
KOLODNY EH, 1973, NEUROLOGY, V23, P427
[10]   STUDIES ON GLUCOSAMINIDASE .4. FLUORIMETRIC ASSAY OF N-ACETYL-BETA-GLUCOSAMINIDASE [J].
LEABACK, DH ;
WALKER, PG .
BIOCHEMICAL JOURNAL, 1961, 78 (01) :151-&