CYSTINOSIS - SELECTIVE INDUCTION OF VACUOLATION IN FIBROBLASTS BY L-CYSTEINE-D-PENICILLAMINE DISULFIDE

被引:18
作者
SCHULMAN, JD
BRADLEY, KH
机构
关键词
D O I
10.1126/science.169.3945.595
中图分类号
O [数理科学和化学]; P [天文学、地球科学]; Q [生物科学]; N [自然科学总论];
学科分类号
07 ; 0710 ; 09 ;
摘要
引用
收藏
页码:595 / &
相关论文
共 15 条
[1]  
BICKEL H, 1952, ACTA PAEDIATR SC S90, V42, P1
[2]  
CHAMBERS RW, 1968, ARCH PATHOL, V85, P18
[3]   CYSTINOSIS IN AN ADULT [J].
COGAN, DG ;
KUWABARA, T ;
KINOSHITA, J ;
SHEEHAN, L ;
MEROLA, L .
JAMA-JOURNAL OF THE AMERICAN MEDICAL ASSOCIATION, 1957, 164 (04) :394-396
[4]   FURTHER OBSERVATIONS ON USE OF D-PENICILLAMINE IN CYSTINURIA [J].
CRAWHALL, JC ;
WATTS, RWE ;
SCOWEN, EF .
BMJ-BRITISH MEDICAL JOURNAL, 1964, 1 (539) :1411-+
[5]   FATE OF PEPTIDES PINOCYTOSED BY MACROPHAGES IN VITRO [J].
EHRENREICH, BA ;
COHN, ZA .
JOURNAL OF EXPERIMENTAL MEDICINE, 1969, 129 (01) :227-+
[6]  
GOLDMAN H, 1970, LANCET, V1, P811
[7]   HUMAN CYSTINOSIS - INTRACELLULAR DEPOSITION OF CYSTINE [J].
HUMMELER, K ;
ZAJAC, BA ;
GENEL, M ;
HOLTZAPPLE, PG ;
SEGAL, S .
SCIENCE, 1970, 168 (3933) :859-+
[8]  
MORECKI R, 1968, ARCH PATHOL, V86, P297
[9]   CYSTINOSIS - ELECTRON MICROSCOPIC EVIDENCE OF LYSOSOMAL STORAGE OF CYSTINE IN LYMPH NODE [J].
PATRICK, AD ;
LAKE, BD .
JOURNAL OF CLINICAL PATHOLOGY, 1968, 21 (05) :571-&
[10]   INCREASED FREE-CYSTINE CONTENT OF FIBROBLASTS CULTURED FROM PATIENTS WITH CYSTINOSIS [J].
SCHNEIDER, JA ;
ROSENBLOOM, FM ;
BRADLEY, KH ;
SEEGMILLER, JE .
BIOCHEMICAL AND BIOPHYSICAL RESEARCH COMMUNICATIONS, 1967, 29 (04) :527-+