CASE OF SEZARY SYNDROME WITH NON-ROSETTING CELLS AND UNUSUAL CYTOGENETIC FINDINGS

被引:6
作者
ADVANI, SH
KHARE, AG
NADKARNI, JJ
BHISEY, AN
NADKARNI, JS
TALVALKAR, GV
机构
[1] Tata Memorial Hospital, Cancer Research Institute, Tata Memorial Centre, Parel, Bombay
关键词
Chromosome; Sézary syndrome; T and B surface markers;
D O I
10.1159/000207655
中图分类号
R5 [内科学];
学科分类号
1002 ; 100201 ;
摘要
A rare case of Sézary syndrome with typical, clinical and haematological picture is described. The absence of any lymphoid surface markers on Sézary cells and the consistent presence of distinct clone 45 XY-F cytogenetic abnormality are very unusual features observed in the present case. In spite of these peculiar findings, response to chlorambucil and prednisolone was excellent. © 1979 S. Karger AG, Basel.
引用
收藏
页码:194 / 197
页数:4
相关论文
共 22 条
[1]   A POPULATION OF LYMPHOCYTES BEARING A MEMBRANE RECEPTOR FOR ANTIGEN-ANTIBODY-COMPLEMENT COMPLEXES .1. SEPARATION AND CHARACTERIZATION [J].
BIANCO, C ;
PATRICK, R ;
NUSSENZWEIG, V .
JOURNAL OF EXPERIMENTAL MEDICINE, 1970, 132 (04) :702-+
[2]  
Boyum A., 1968, SCAND J CLIN LAB INV, V97, P7
[3]   SEZARY SYNDROME LYMPHOID-CELL - ABNORMAL SURFACE PROPERTIES AND MITOGEN RESPONSIVENESS [J].
BRAYLAN, R ;
VARIAKOJIS, D ;
YACHNIN, S .
BRITISH JOURNAL OF HAEMATOLOGY, 1975, 31 (04) :553-&
[4]   SEZARY SYNDROME - MALIGNANT PROLIFERATION OF HELPER T CELLS [J].
BRODER, S ;
EDELSON, RL ;
LUTZNER, MA ;
NELSON, DL ;
MACDERMOTT, RP ;
DURM, ME ;
GOLDMAN, CK ;
MEADE, BD ;
WALDMANN, TA .
JOURNAL OF CLINICAL INVESTIGATION, 1976, 58 (06) :1297-1306
[5]   INDICATIONS OF THYMUS-DERIVED NATURE OF PROLIFERATING CELLS IN 6 PATIENTS WITH SEZARYS SYNDROME [J].
BROUET, JC ;
FLANDRIN, G ;
SELIGMANN, M .
NEW ENGLAND JOURNAL OF MEDICINE, 1973, 289 (07) :341-344
[6]   MYCOSIS FUNGOIDES - RELATIONSHIP TO MALIGNANT CUTANEOUS RETICULOSIS + SEZARY SYNDROME [J].
CLENDENNING, WE ;
BRECHER, G ;
VANSCOTT, EJ .
ARCHIVES OF DERMATOLOGY, 1964, 89 (06) :785-+
[7]   SEZARY SYNDROME - CYTOGENETIC STUDIES AND IDENTIFICATION OF SEZARY CELL AS AN ABNORMAL LYMPHOCYTE [J].
CROSSEN, PE ;
MELLOR, JEL ;
FINLEY, AG ;
RAVICH, RBM ;
VINCENT, PC ;
GUNZ, FW .
AMERICAN JOURNAL OF MEDICINE, 1971, 50 (01) :24-&
[8]  
DEWALD G, 1974, MAYO CLIN PROC, V49, P553
[9]   PREFERENTIAL CUTANEOUS INFILTRATION BY NEOPLASTIC THYMUS-DERIVED LYMPHOCYTES - MORPHOLOGIC AND FUNCTIONAL STUDIES [J].
EDELSON, RL ;
KIRKPATRICK, CH ;
SHEVACH, EM ;
SCHEIN, PS ;
SMITH, RW ;
GREEN, I ;
LUTZNER, M .
ANNALS OF INTERNAL MEDICINE, 1974, 80 (06) :685-692
[10]  
FLANDRIN G, 1974, MAYO CLIN PROC, V49, P575