INTRAVASCULAR LYMPHOMATOSIS - A CLINICOPATHOLOGICAL STUDY OF 3 CASES

被引:17
作者
LISZKA, U
DRLICEK, M
HITZENBERGER, P
MACHACEK, E
MAYER, H
STOCKHAMMER, G
GRISOLD, W
机构
[1] UNIV INNSBRUCK, DEPT PATHOL, A-6020 INNSBRUCK, AUSTRIA
[2] KAISER FRANZ JOSEF SPITAL, DEPT PATHOL, VIENNA, AUSTRIA
[3] LUDWIG BOLTZMANN INST CLIN NEUROBIOL, VIENNA, AUSTRIA
[4] KAISER FRANZ JOSEF SPITAL, DEPT NEUROL, VIENNA, AUSTRIA
[5] UNIV INNSBRUCK, DEPT NEUROL, A-6020 INNSBRUCK, AUSTRIA
关键词
INTRAVASCULAR MALIGNANT LYMPHOMA; B-CELL LYMPHOMA; MALIGNANT ANGIOENDOTHELIOMATOSIS; CNS INVOLVEMENT; BRAIN BIOPSY;
D O I
10.1007/BF01202196
中图分类号
R73 [肿瘤学];
学科分类号
100214 ;
摘要
In patients with intravascular lymphomatosis (IL) a broad spectrum of neuro-psychiatric disorders including dementia, focal neurological signs and seizures has been reported. Clinical diagnosis is difficult since neuroimaging findings are nonspecific. The clinical histories, biopsy and autopsy findings of three patients with IL, one with brain biopsy, are described. Two of them presented with rapidly progressive, fluctuating dementia. The third patient suffered from seizures followed by aphasia. Histology revealed large-cell lymphoma of the B cell type. The prognosis of IL, in general, is poor.
引用
收藏
页码:164 / 168
页数:5
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